Medical Subject Headings

Last uploaded: January 31, 2024
Preferred Name

Leukoencephalitis, Acute Hemorrhagic

Synonyms

Hurst Syndrome

Definitions

A fulminant and often fatal demyelinating disease of the brain which primarily affects young adults and children. Clinical features include the rapid onset of weakness, SEIZURES, and COMA. It may follow a viral illness or MYCOPLASMA PNEUMONIAE infections but in most instances there is no precipitating event. Pathologic examination reveals marked perivascular demyelination and necrosis of white matter with microhemorrhages. (Adams et al., Principles of Neurology, 6th ed, pp924-5)

ID

http://purl.bioontology.org/ontology/MESH/D004684

altLabel

Hurst Syndrome

Encephalomyelitis, Acute Hemorrhagic

Acute Hemorrhagic Leukoencephalitis

Acute Necrotizing Encephalitis

Hurst Disease

Hemorrhagic Encephalomyelitides, Acute

Subacute Hemorrhagic Leukoencephalitides

Necrotizing Hemorrhagic Encephalomyelitides

Disease, Hurst's

Necrotizing Encephalitis, Acute

Hemorrhagic Encephalomyelitides, Necrotizing

Encephalomyelitis, Hemorrhagic Necrotizing

Leukoencephalitis, Subacute Hemorrhagic

Necrotizing Hemorrhagic Encephalomyelitis

Hemorrhagic Leukoencephalitis, Subacute

Necrotizing Encephalomyelitides, Hemorrhagic

Subacute Hemorrhagic Leukoencephalitis

Acute Hemorrhagic Leukoencephalitides

Hurst's Disease

Necrotizing Encephalitides, Acute

Encephalomyelitides, Hemorrhagic Necrotizing

Acute Necrotizing Encephalitides

Hemorrhagic Leukoencephalitides, Subacute

Necrotizing Encephalomyelitis, Hemorrhagic

Leukoencephalitides, Subacute Hemorrhagic

Acute Hemorrhagic Encephalomyelitides

Hemorrhagic Leukoencephalitis, Acute

Encephalomyelitis, Necrotizing Hemorrhagic

Encephalomyelitis, Acute Necrotizing Hemorrhagic

Encephalitides, Acute Necrotizing

Acute Hemorrhagic Encephalomyelitis

Encephalomyelitides, Acute Hemorrhagic

Hemorrhagic Leukoencephalitides, Acute

Disease, Hurst

Syndrome, Hurst

Leukoencephalitides, Acute Hemorrhagic

Encephalitis, Acute Necrotizing

Leukoencephalitis Acuta Hemorrhagica

Hemorrhagic Necrotizing Encephalomyelitis

Hursts Disease

Hemorrhagic Encephalomyelitis, Necrotizing

Hemorrhagic Encephalomyelitis, Acute

AQL

BL CF CI CL CN CO DG DH DI DT EC EH EM EN EP ET GE HI IM ME MI MO NU PA PC PP PS PX RH RT SU TH UR VE VI

cui

C0751108

C0338418

C0014077

C0376171

DC

1

definition

A fulminant and often fatal demyelinating disease of the brain which primarily affects young adults and children. Clinical features include the rapid onset of weakness, SEIZURES, and COMA. It may follow a viral illness or MYCOPLASMA PNEUMONIAE infections but in most instances there is no precipitating event. Pathologic examination reveals marked perivascular demyelination and necrosis of white matter with microhemorrhages. (Adams et al., Principles of Neurology, 6th ed, pp924-5)

DX

19910101

HN

1997; was ENCEPHALOMYELITIS, NECROTIZING HEMORRHAGIC 1991-1996 (see under ENCEPHALOMYELITIS 1972-1990); HURST DISEASE was HURST'S DISEASE 1997

Inverse of AQ

http://purl.bioontology.org/ontology/MESH/Q000097

http://purl.bioontology.org/ontology/MESH/Q000178

http://purl.bioontology.org/ontology/MESH/Q000175

http://purl.bioontology.org/ontology/MESH/Q000628

http://purl.bioontology.org/ontology/MESH/Q000276

http://purl.bioontology.org/ontology/MESH/Q000134

http://purl.bioontology.org/ontology/MESH/Q000139

http://purl.bioontology.org/ontology/MESH/Q000266

http://purl.bioontology.org/ontology/MESH/Q000378

http://purl.bioontology.org/ontology/MESH/Q000517

http://purl.bioontology.org/ontology/MESH/Q000662

http://purl.bioontology.org/ontology/MESH/Q000469

http://purl.bioontology.org/ontology/MESH/Q000151

http://purl.bioontology.org/ontology/MESH/Q000150

http://purl.bioontology.org/ontology/MESH/Q000821

http://purl.bioontology.org/ontology/MESH/Q000191

http://purl.bioontology.org/ontology/MESH/Q000196

http://purl.bioontology.org/ontology/MESH/Q000473

http://purl.bioontology.org/ontology/MESH/Q000145

http://purl.bioontology.org/ontology/MESH/Q000382

http://purl.bioontology.org/ontology/MESH/Q000451

http://purl.bioontology.org/ontology/MESH/Q000453

http://purl.bioontology.org/ontology/MESH/Q000534

http://purl.bioontology.org/ontology/MESH/Q000532

http://purl.bioontology.org/ontology/MESH/Q000503

http://purl.bioontology.org/ontology/MESH/Q000188

http://purl.bioontology.org/ontology/MESH/Q000235

http://purl.bioontology.org/ontology/MESH/Q000201

http://purl.bioontology.org/ontology/MESH/Q000209

http://purl.bioontology.org/ontology/MESH/Q000208

http://purl.bioontology.org/ontology/MESH/Q000601

http://purl.bioontology.org/ontology/MESH/Q000000981

http://purl.bioontology.org/ontology/MESH/Q000652

http://purl.bioontology.org/ontology/MESH/Q000523

http://purl.bioontology.org/ontology/MESH/Q000401

Machine permutation

1997; was ENCEPHALOMYELITIS, NECROTIZING HEMORRHAGIC 1991-1996 (see under ENCEPHALOMYELITIS 1972-1990); HURST DISEASE was HURST'S DISEASE 1997

MDA

19990101

MMR

20220714

MN

C10.314.350.225.500

C20.111.258.250.350.500

C10.228.140.695.562.225.500

C10.114.375.225.500

notation

D004684

prefLabel

Leukoencephalitis, Acute Hemorrhagic

TERMUI

T014361

T811516

T014367

T000878009

T014357

T366415

T014360

T366416

T014362

T014364

T014366

T014356

T014358

T014363

T014365

T014359

TH

NLM (1997)

NLM (2016)

OMIM (2013)

NLM (1971)

NLM (2000)

NLM (1995)

NLM (1998)

ORD (2010)

tui

T047

subClassOf

http://purl.bioontology.org/ontology/MESH/D004673

Delete Subject Author Type Created
No notes to display
Create mapping

Delete Mapping To Ontology Source
http://purl.bioontology.org/ontology/MSHFRE/D004684 MSHFRE CUI
http://purl.bioontology.org/ontology/MSHFRE/D004684 MSHFRE CUI
http://purl.bioontology.org/ontology/MEDDRA/10058993 MEDDRA CUI
http://purl.bioontology.org/ontology/MSHFRE/D004684 MSHFRE CUI
http://purl.bioontology.org/ontology/RCD/X005h RCD CUI
http://purl.bioontology.org/ontology/RCD/A4zy1 RCD CUI
http://purl.bioontology.org/ontology/SNOMEDCT/111897007 SNOMEDCT CUI
http://purl.bioontology.org/ontology/SCTSPA/111897007 SCTSPA CUI
http://purl.bioontology.org/ontology/MDRGER/10058994 MDRGER CUI
http://purl.bioontology.org/ontology/MDRFRE/10058993 MDRFRE CUI
http://purl.bioontology.org/ontology/SNOMEDCT/72986009 SNOMEDCT CUI
http://purl.bioontology.org/ontology/MSHFRE/D004684 MSHFRE CUI
http://purl.bioontology.org/ontology/MEDDRA/10058994 MEDDRA CUI
http://purl.bioontology.org/ontology/RCD/X001P RCD CUI
http://purl.bioontology.org/ontology/MDRGER/10058993 MDRGER CUI
http://purl.bioontology.org/ontology/SNMI/DA-10540 SNMI CUI
http://purl.bioontology.org/ontology/NDFRT/N0000001089 NDFRT CUI
http://purl.bioontology.org/ontology/MDRFRE/10058994 MDRFRE CUI
http://purl.bioontology.org/ontology/OMIM/606752 OMIM CUI
http://purl.bioontology.org/ontology/SCTSPA/72986009 SCTSPA CUI
http://phenomebrowser.net/ontologies/mesh/mesh.owl#C10.114.375.362 RH-MESH LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#C20.111.258.250.425 RH-MESH LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#C10.114.562 RH-MESH LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#C20.111.258.450 RH-MESH LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#C10.228.440.650 RH-MESH LOOM
http://purl.jp/bio/4/id/200906051323427917 IOBC LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#C10.228.140.695.562.375 RH-MESH LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#C10.314.350.375 RH-MESH LOOM
http://purl.obolibrary.org/obo/OMIT_0005928 OMIT LOOM
http://www.phoc.org.cn/pmo/class/PMO_00038366 PMAPP-PMO LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#C10.228.228.245.670 RH-MESH LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#D004684 RH-MESH LOOM