Medical Subject Headings

Last uploaded: January 31, 2024
Preferred Name

Persistent Fetal Circulation Syndrome

Synonyms

ACD MPV

Familial Persistent Pulmonary Hypertension of the Newborn

Persistent Pulmonary Hypertension of Newborn

Alveolar Capillary Dysplasia With Misalignment Of Pulmonary Veins

ACDMPV

Hypertension, Pulmonary, of Newborn, Persistent

Fetal Circulation, Persistent

Alveolar Capillary Dysplasia With Misalignment Of Pulmonary Veins And Other Congenital Anomalies

Circulation, Persistent Fetal

Pulmonary Hypertension, Familial Persistent, of the Newborn

Misalignment of the Pulmonary Vessels

ACD-MPV

Persistent Fetal Circulation

Definitions

A syndrome of persistent PULMONARY HYPERTENSION in the newborn infant (INFANT, NEWBORN) without demonstrable HEART DISEASES. This neonatal condition can be caused by severe pulmonary vasoconstriction (reactive type), hypertrophy of pulmonary arterial muscle (hypertrophic type), or abnormally developed pulmonary arterioles (hypoplastic type). The newborn patient exhibits CYANOSIS and ACIDOSIS due to the persistence of fetal circulatory pattern of right-to-left shunting of blood through a patent ductus arteriosus (DUCTUS ARTERIOSUS, PATENT) and at times a patent foramen ovale (FORAMEN OVALE, PATENT).

ID

http://purl.bioontology.org/ontology/MESH/D010547

altLabel

ACD MPV

Familial Persistent Pulmonary Hypertension of the Newborn

Persistent Pulmonary Hypertension of Newborn

Alveolar Capillary Dysplasia With Misalignment Of Pulmonary Veins

ACDMPV

Hypertension, Pulmonary, of Newborn, Persistent

Fetal Circulation, Persistent

Alveolar Capillary Dysplasia With Misalignment Of Pulmonary Veins And Other Congenital Anomalies

Circulation, Persistent Fetal

Pulmonary Hypertension, Familial Persistent, of the Newborn

Misalignment of the Pulmonary Vessels

ACD-MPV

Persistent Fetal Circulation

AN

also known as PPHN check the tags HUMANS & INFANT, NEWBORN

AQL

BL CF CI CL CO DG DH DI DT EC EH EM EN EP ET GE HI IM ME MI MO NU PA PC PP PS PX RH RT SU TH UR VE VI

cui

C0031190

DC

1

definition

A syndrome of persistent PULMONARY HYPERTENSION in the newborn infant (INFANT, NEWBORN) without demonstrable HEART DISEASES. This neonatal condition can be caused by severe pulmonary vasoconstriction (reactive type), hypertrophy of pulmonary arterial muscle (hypertrophic type), or abnormally developed pulmonary arterioles (hypoplastic type). The newborn patient exhibits CYANOSIS and ACIDOSIS due to the persistence of fetal circulatory pattern of right-to-left shunting of blood through a patent ductus arteriosus (DUCTUS ARTERIOSUS, PATENT) and at times a patent foramen ovale (FORAMEN OVALE, PATENT).

DX

19800101

FX

D004374

HN

1980

Inverse of AQ

http://purl.bioontology.org/ontology/MESH/Q000097

http://purl.bioontology.org/ontology/MESH/Q000178

http://purl.bioontology.org/ontology/MESH/Q000175

http://purl.bioontology.org/ontology/MESH/Q000628

http://purl.bioontology.org/ontology/MESH/Q000276

http://purl.bioontology.org/ontology/MESH/Q000134

http://purl.bioontology.org/ontology/MESH/Q000139

http://purl.bioontology.org/ontology/MESH/Q000266

http://purl.bioontology.org/ontology/MESH/Q000378

http://purl.bioontology.org/ontology/MESH/Q000517

http://purl.bioontology.org/ontology/MESH/Q000662

http://purl.bioontology.org/ontology/MESH/Q000469

http://purl.bioontology.org/ontology/MESH/Q000150

http://purl.bioontology.org/ontology/MESH/Q000821

http://purl.bioontology.org/ontology/MESH/Q000191

http://purl.bioontology.org/ontology/MESH/Q000196

http://purl.bioontology.org/ontology/MESH/Q000473

http://purl.bioontology.org/ontology/MESH/Q000145

http://purl.bioontology.org/ontology/MESH/Q000382

http://purl.bioontology.org/ontology/MESH/Q000451

http://purl.bioontology.org/ontology/MESH/Q000453

http://purl.bioontology.org/ontology/MESH/Q000534

http://purl.bioontology.org/ontology/MESH/Q000532

http://purl.bioontology.org/ontology/MESH/Q000503

http://purl.bioontology.org/ontology/MESH/Q000188

http://purl.bioontology.org/ontology/MESH/Q000235

http://purl.bioontology.org/ontology/MESH/Q000201

http://purl.bioontology.org/ontology/MESH/Q000209

http://purl.bioontology.org/ontology/MESH/Q000208

http://purl.bioontology.org/ontology/MESH/Q000601

http://purl.bioontology.org/ontology/MESH/Q000000981

http://purl.bioontology.org/ontology/MESH/Q000652

http://purl.bioontology.org/ontology/MESH/Q000523

http://purl.bioontology.org/ontology/MESH/Q000401

Inverse of RO

http://purl.bioontology.org/ontology/MESH/D004374

Machine permutation

1980

Mapped from

http://purl.bioontology.org/ontology/MESH/C536590

MDA

19790228

MMR

20130708

MN

C16.614.694

C08.381.423.694

notation

D010547

prefLabel

Persistent Fetal Circulation Syndrome

TERMUI

T031139

T031140

T031143

T840885

T811823

T840884

T843553

T031138

T031142

T031141

T843554

T753016

T811822

TH

OMIM (2013)

NLM (1994)

UNK (19XX)

NLM (2010)

GHR (2014)

NLM (1980)

ORD (2010)

tui

T047

subClassOf

http://purl.bioontology.org/ontology/MESH/D007232

http://purl.bioontology.org/ontology/MESH/D006976

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Delete Mapping To Ontology Source
http://purl.bioontology.org/ontology/OMIM/265380 OMIM CUI
http://purl.bioontology.org/ontology/MDRGER/10034709 MDRGER CUI
http://purl.bioontology.org/ontology/ICD10CM/P29.3 ICD10CM CUI
http://purl.bioontology.org/ontology/ICD10CM/P29.30 ICD10CM CUI
http://purl.bioontology.org/ontology/MDRFRE/10054726 MDRFRE CUI
http://purl.bioontology.org/ontology/NDFRT/N0000002380 NDFRT CUI
http://purl.bioontology.org/ontology/OMIM/MTHU046520 OMIM CUI
http://purl.bioontology.org/ontology/CSP/0723-5955 CRISP CUI
http://purl.bioontology.org/ontology/SNOMEDCT/233815004 SNOMEDCT CUI
http://purl.bioontology.org/ontology/ICD9CM/747.83 ICD9CM CUI
http://purl.bioontology.org/ontology/MDRGER/10034708 MDRGER CUI
http://purl.bioontology.org/ontology/ICPC2P/A94023 ICPC2P CUI
http://purl.bioontology.org/ontology/MDRFRE/10053592 MDRFRE CUI
http://purl.bioontology.org/ontology/MDRFRE/10034709 MDRFRE CUI
http://purl.bioontology.org/ontology/MEDDRA/10083882 MEDDRA CUI
http://purl.bioontology.org/ontology/MSHFRE/D010547 MSHFRE CUI
http://purl.bioontology.org/ontology/MEDDRA/10053592 MEDDRA CUI
http://purl.bioontology.org/ontology/SCTSPA/233815004 SCTSPA CUI
http://purl.bioontology.org/ontology/MDRFRE/10083882 MDRFRE CUI
http://purl.bioontology.org/ontology/MEDDRA/10034709 MEDDRA CUI
http://purl.bioontology.org/ontology/MDRFRE/10034708 MDRFRE CUI
http://purl.bioontology.org/ontology/MDRGER/10054726 MDRGER CUI
http://purl.bioontology.org/ontology/MEDDRA/10054726 MEDDRA CUI
http://purl.bioontology.org/ontology/SNMI/D4-30010 SNMI CUI
http://purl.bioontology.org/ontology/RCD/X2001 RCD CUI
http://purl.bioontology.org/ontology/MDRFRE/10082195 MDRFRE CUI
http://purl.bioontology.org/ontology/OMIM/MTHU070849 OMIM CUI
http://purl.bioontology.org/ontology/MDRGER/10053592 MDRGER CUI
http://purl.bioontology.org/ontology/MDRGER/10083882 MDRGER CUI
http://purl.bioontology.org/ontology/OMIM/601089 OMIM CUI
http://purl.bioontology.org/ontology/ICD10/P29.3 ICD10 CUI
http://purl.bioontology.org/ontology/MEDDRA/10034708 MEDDRA CUI
http://purl.bioontology.org/ontology/CSP/2595-6954 CRISP CUI
http://purl.bioontology.org/ontology/MDRGER/10082195 MDRGER CUI
http://purl.bioontology.org/ontology/MEDDRA/10082195 MEDDRA CUI
http://purl.obolibrary.org/obo/DOID_13042 DOID LOOM
http://www.ebi.ac.uk/efo/EFO_1001103 EFO LOOM
http://purl.obolibrary.org/obo/MONDO_0022430 MONDO LOOM
http://purl.obolibrary.org/obo/DOID_13042 DOID LOOM
http://purl.obolibrary.org/obo/OMIT_0011538 OMIT LOOM
http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#Persistent_Fetal_Circulation_Syndrome CSEO LOOM
http://purl.jp/bio/4/id/200906044982385303 IOBC LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#C16.614.694 RH-MESH LOOM
http://www.owl-ontologies.com/NPOntology.owl#DOID_13042 NATPRO LOOM
http://purl.obolibrary.org/obo/MONDO_0022430 DOVES LOOM
http://id.nlm.nih.gov/mesh/D010547 MDM LOOM
http://www.phoc.org.cn/pmo/class/PMO_00039142 PMAPP-PMO LOOM
http://purl.bioontology.org/ontology/SNMI/D4-30010 SNMI LOOM
http://www.limics.fr/ontologies/ontolurgences#SyndromeDeCirculationFoetalePersistante ONTOLURGENCES LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#C08.381.423.694 RH-MESH LOOM
http://purl.obolibrary.org/obo/DOID_13042 BAO LOOM
http://purl.obolibrary.org/obo/DOID_13042 HHEAR LOOM
http://purl.obolibrary.org/obo/DOID_13042 NIFSTD LOOM
http://purl.obolibrary.org/obo/DOID_13042 MIDO LOOM
http://purl.obolibrary.org/obo/DOID_13042 FNS-H LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#D010547 RH-MESH LOOM