Medical Subject Headings

Last uploaded: January 31, 2024
Preferred Name

Scleroderma, Systemic

Synonyms

Systemic Sclerosis

Sclerosis, Systemic

Definitions

A chronic multi-system disorder of CONNECTIVE TISSUE. It is characterized by SCLEROSIS in the SKIN, the LUNGS, the HEART, the GASTROINTESTINAL TRACT, the KIDNEYS, and the MUSCULOSKELETAL SYSTEM. Other important features include diseased small BLOOD VESSELS and AUTOANTIBODIES. The disorder is named for its most prominent feature (hard skin), and classified into subsets by the extent of skin thickening: LIMITED SCLERODERMA and DIFFUSE SCLERODERMA.

ID

http://purl.bioontology.org/ontology/MESH/D012595

altLabel

Systemic Sclerosis

Systemic Scleroderma

Sclerosis, Systemic

AN

note specific indentations and SCLERODERMA, LOCALIZED

AQL

BL CF CI CL CN CO DG DH DI DT EC EH EM EN EP ET GE HI IM ME MI MO NU PA PC PP PS PX RH RT SU TH UR VE VI

cui

C0036421

DC

1

definition

A chronic multi-system disorder of CONNECTIVE TISSUE. It is characterized by SCLEROSIS in the SKIN, the LUNGS, the HEART, the GASTROINTESTINAL TRACT, the KIDNEYS, and the MUSCULOSKELETAL SYSTEM. Other important features include diseased small BLOOD VESSELS and AUTOANTIBODIES. The disorder is named for its most prominent feature (hard skin), and classified into subsets by the extent of skin thickening: LIMITED SCLERODERMA and DIFFUSE SCLERODERMA.

DX

19710101

HN

1971

Inverse of AQ

http://purl.bioontology.org/ontology/MESH/Q000097

http://purl.bioontology.org/ontology/MESH/Q000178

http://purl.bioontology.org/ontology/MESH/Q000175

http://purl.bioontology.org/ontology/MESH/Q000628

http://purl.bioontology.org/ontology/MESH/Q000276

http://purl.bioontology.org/ontology/MESH/Q000134

http://purl.bioontology.org/ontology/MESH/Q000139

http://purl.bioontology.org/ontology/MESH/Q000266

http://purl.bioontology.org/ontology/MESH/Q000378

http://purl.bioontology.org/ontology/MESH/Q000517

http://purl.bioontology.org/ontology/MESH/Q000662

http://purl.bioontology.org/ontology/MESH/Q000469

http://purl.bioontology.org/ontology/MESH/Q000151

http://purl.bioontology.org/ontology/MESH/Q000150

http://purl.bioontology.org/ontology/MESH/Q000821

http://purl.bioontology.org/ontology/MESH/Q000191

http://purl.bioontology.org/ontology/MESH/Q000196

http://purl.bioontology.org/ontology/MESH/Q000473

http://purl.bioontology.org/ontology/MESH/Q000145

http://purl.bioontology.org/ontology/MESH/Q000382

http://purl.bioontology.org/ontology/MESH/Q000451

http://purl.bioontology.org/ontology/MESH/Q000453

http://purl.bioontology.org/ontology/MESH/Q000534

http://purl.bioontology.org/ontology/MESH/Q000532

http://purl.bioontology.org/ontology/MESH/Q000503

http://purl.bioontology.org/ontology/MESH/Q000188

http://purl.bioontology.org/ontology/MESH/Q000235

http://purl.bioontology.org/ontology/MESH/Q000201

http://purl.bioontology.org/ontology/MESH/Q000209

http://purl.bioontology.org/ontology/MESH/Q000208

http://purl.bioontology.org/ontology/MESH/Q000601

http://purl.bioontology.org/ontology/MESH/Q000000981

http://purl.bioontology.org/ontology/MESH/Q000652

http://purl.bioontology.org/ontology/MESH/Q000523

http://purl.bioontology.org/ontology/MESH/Q000401

Machine permutation

1971; SCLERODERMA was heading 1963-70

Mapped from

http://purl.bioontology.org/ontology/MESH/C537703

http://purl.bioontology.org/ontology/MESH/C543759

MDA

19990101

MMR

20130708

MN

C17.300.799

C17.800.784

notation

D012595

prefLabel

Scleroderma, Systemic

TERMUI

T037317

T540313

T037315

T540315

TH

NLM (1997)

NLM (2004)

NLM (1971)

GHR (2014)

tui

T047

subClassOf

http://purl.bioontology.org/ontology/MESH/D003240

http://purl.bioontology.org/ontology/MESH/D012871

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Delete Mapping To Ontology Source
http://purl.bioontology.org/ontology/RCD/Xa1jE RCD CUI
http://purl.bioontology.org/ontology/CSP/4008-0097 CRISP CUI
http://purl.bioontology.org/ontology/ICD9CM/710.1 ICD9CM CUI
http://purl.bioontology.org/ontology/SCTSPA/89155008 SCTSPA CUI
http://purl.bioontology.org/ontology/MEDDRA/10036814 MEDDRA CUI
http://purl.bioontology.org/ontology/ICD10CM/M34.0 ICD10CM CUI
http://purl.bioontology.org/ontology/MEDDRA/10042953 MEDDRA CUI
http://purl.bioontology.org/ontology/ICD10/M34.0 ICD10 CUI
http://purl.bioontology.org/ontology/SNMI/D1-10200 SNMI CUI
http://purl.bioontology.org/ontology/MDRFRE/10036814 MDRFRE CUI
http://purl.bioontology.org/ontology/MDRGER/10078638 MDRGER CUI
http://purl.bioontology.org/ontology/MDRFRE/10078638 MDRFRE CUI
http://purl.bioontology.org/ontology/AIR/PSS AI-RHEUM CUI
http://purl.bioontology.org/ontology/AIR/DXPSS AI-RHEUM CUI
http://purl.bioontology.org/ontology/ICPC2P/L99071 ICPC2P CUI
http://purl.bioontology.org/ontology/SNOMEDCT/89155008 SNOMEDCT CUI
http://purl.bioontology.org/ontology/MEDLINEPLUS/C0036421 MEDLINEPLUS CUI
http://purl.bioontology.org/ontology/PDQ/CDR0000587622 PDQ CUI
http://purl.bioontology.org/ontology/MDRGER/10036814 MDRGER CUI
http://purl.bioontology.org/ontology/MSHFRE/D012595 MSHFRE CUI
http://purl.bioontology.org/ontology/MDRGER/10042953 MDRGER CUI
http://purl.bioontology.org/ontology/MEDDRA/10078638 MEDDRA CUI
http://purl.bioontology.org/ontology/NDFRT/N0000002701 NDFRT CUI
http://purl.bioontology.org/ontology/ICD10/M34 ICD10 CUI
http://purl.bioontology.org/ontology/ICD10/M34.9 ICD10 CUI
http://purl.bioontology.org/ontology/ICPC2P/L99028 ICPC2P CUI
http://purl.bioontology.org/ontology/ICD10CM/M34.9 ICD10CM CUI
http://purl.bioontology.org/ontology/MDRFRE/10042953 MDRFRE CUI
http://phenomebrowser.net/ontologies/mesh/mesh.owl#C17.800.784 RH-MESH LOOM
http://purl.obolibrary.org/obo/OMIT_0013497 OMIT LOOM
http://www.phoc.org.cn/pmo/class/PMO_00039249 PMAPP-PMO LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#D012595 RH-MESH LOOM
http://id.nlm.nih.gov/mesh/D012595 MDM LOOM
http://purl.jp/bio/4/id/200906086636185084 IOBC LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#C17.300.799 RH-MESH LOOM