Medical Subject Headings

Last uploaded: January 31, 2024
Preferred Name

Sarcoma, Alveolar Soft Part

Synonyms

Alveolar Soft-Part Sarcoma

Alveolar Soft Part Sarcoma

Definitions

A variety of rare sarcoma having a reticulated fibrous stroma enclosing groups of sarcoma cells, which resemble epithelial cells and are enclosed in alveoli walled with connective tissue. It is a rare tumor, usually occurring between 15 and 35 years of age. It appears in the muscles of the extremities in adults and most commonly in the head and neck regions of children. Though slow-growing, it commonly metastasizes to the lungs, brain, bones, and lymph nodes. (DeVita Jr et al., Cancer: Principles & Practice of Oncology, 3d ed, p1365)

ID

http://purl.bioontology.org/ontology/MESH/D018234

altLabel

Alveolar Soft-Part Sarcoma

Alveolar Soft Part Sarcoma

AN

"alveolar" has nothing to do with pulmonary alveoli: it refers to sac-like pathology of soft part; coordinate with precoordinated organ/neoplasm term

AQL

BL BS CF CH CI CL CN CO DG DH DI DT EC EH EM EN EP ET GE HI IM ME MI MO NU PA PC PP PS PX RH RT SC SU TH UL UR VE VI

cui

C0206657

DC

1

definition

A variety of rare sarcoma having a reticulated fibrous stroma enclosing groups of sarcoma cells, which resemble epithelial cells and are enclosed in alveoli walled with connective tissue. It is a rare tumor, usually occurring between 15 and 35 years of age. It appears in the muscles of the extremities in adults and most commonly in the head and neck regions of children. Though slow-growing, it commonly metastasizes to the lungs, brain, bones, and lymph nodes. (DeVita Jr et al., Cancer: Principles & Practice of Oncology, 3d ed, p1365)

DX

19940101

HN

1994

Inverse of AQ

http://purl.bioontology.org/ontology/MESH/Q000097

http://purl.bioontology.org/ontology/MESH/Q000098

http://purl.bioontology.org/ontology/MESH/Q000178

http://purl.bioontology.org/ontology/MESH/Q000175

http://purl.bioontology.org/ontology/MESH/Q000628

http://purl.bioontology.org/ontology/MESH/Q000648

http://purl.bioontology.org/ontology/MESH/Q000276

http://purl.bioontology.org/ontology/MESH/Q000134

http://purl.bioontology.org/ontology/MESH/Q000139

http://purl.bioontology.org/ontology/MESH/Q000266

http://purl.bioontology.org/ontology/MESH/Q000378

http://purl.bioontology.org/ontology/MESH/Q000517

http://purl.bioontology.org/ontology/MESH/Q000662

http://purl.bioontology.org/ontology/MESH/Q000469

http://purl.bioontology.org/ontology/MESH/Q000151

http://purl.bioontology.org/ontology/MESH/Q000150

http://purl.bioontology.org/ontology/MESH/Q000821

http://purl.bioontology.org/ontology/MESH/Q000191

http://purl.bioontology.org/ontology/MESH/Q000196

http://purl.bioontology.org/ontology/MESH/Q000473

http://purl.bioontology.org/ontology/MESH/Q000145

http://purl.bioontology.org/ontology/MESH/Q000737

http://purl.bioontology.org/ontology/MESH/Q000382

http://purl.bioontology.org/ontology/MESH/Q000451

http://purl.bioontology.org/ontology/MESH/Q000453

http://purl.bioontology.org/ontology/MESH/Q000534

http://purl.bioontology.org/ontology/MESH/Q000532

http://purl.bioontology.org/ontology/MESH/Q000503

http://purl.bioontology.org/ontology/MESH/Q000188

http://purl.bioontology.org/ontology/MESH/Q000235

http://purl.bioontology.org/ontology/MESH/Q000201

http://purl.bioontology.org/ontology/MESH/Q000209

http://purl.bioontology.org/ontology/MESH/Q000208

http://purl.bioontology.org/ontology/MESH/Q000601

http://purl.bioontology.org/ontology/MESH/Q000000981

http://purl.bioontology.org/ontology/MESH/Q000556

http://purl.bioontology.org/ontology/MESH/Q000652

http://purl.bioontology.org/ontology/MESH/Q000523

http://purl.bioontology.org/ontology/MESH/Q000401

Machine permutation

1994

MDA

19930625

MMR

20120703

MN

C04.557.450.795.775

C04.557.450.590.775

notation

D018234

prefLabel

Sarcoma, Alveolar Soft Part

TERMUI

T812104

T054511

T752461

TH

OMIM (2013)

NLM (1994)

NLM (2010)

ORD (2010)

tui

T191

subClassOf

http://purl.bioontology.org/ontology/MESH/D009379

http://purl.bioontology.org/ontology/MESH/D012509

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http://purl.bioontology.org/ontology/MDRFRE/10001883 MDRFRE CUI
http://purl.bioontology.org/ontology/MEDDRA/10001882 MEDDRA CUI
http://purl.bioontology.org/ontology/SNOMEDCT/88195001 SNOMEDCT CUI
http://purl.bioontology.org/ontology/NDFRT/N0000003708 NDFRT CUI
http://purl.bioontology.org/ontology/MDRFRE/10001882 MDRFRE CUI
http://purl.bioontology.org/ontology/MEDDRA/10001883 MEDDRA CUI
http://purl.bioontology.org/ontology/MDRFRE/10001886 MDRFRE CUI
http://purl.bioontology.org/ontology/MEDDRA/10001886 MEDDRA CUI
http://purl.bioontology.org/ontology/MDRGER/10001886 MDRGER CUI
http://purl.bioontology.org/ontology/SNOMEDCT/404056007 SNOMEDCT CUI
http://purl.bioontology.org/ontology/SCTSPA/88195001 SCTSPA CUI
http://purl.bioontology.org/ontology/OMIM/606243 OMIM CUI
http://purl.bioontology.org/ontology/MSHFRE/D018234 MSHFRE CUI
http://purl.bioontology.org/ontology/SNMI/M-95813 SNMI CUI
http://purl.bioontology.org/ontology/SCTSPA/404056007 SCTSPA CUI
http://purl.bioontology.org/ontology/MDRGER/10001883 MDRGER CUI
http://purl.bioontology.org/ontology/MDRGER/10001882 MDRGER CUI
http://purl.bioontology.org/ontology/RCD/Xa99f RCD CUI
http://purl.jp/bio/4/id/200906010649654362 IOBC LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#D018234 RH-MESH LOOM
http://id.nlm.nih.gov/mesh/D018234 MDM LOOM
http://www.phoc.org.cn/pmo/class/PMO_00037878 PMAPP-PMO LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#C04.557.450.795.775 RH-MESH LOOM
http://purl.obolibrary.org/obo/OMIT_0018467 OMIT LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#C04.557.450.590.775 RH-MESH LOOM