Medical Subject Headings

Last uploaded: January 31, 2024
Preferred Name

Landau-Kleffner Syndrome

Synonyms

Landau Kleffner Acquired Epileptiform Aphasia

Definitions

A syndrome characterized by the onset of isolated language dysfunction in otherwise normal children (age of onset 4-7 years) and epileptiform discharges on ELECTROENCEPHALOGRAPHY. Seizures, including atypical absence (EPILEPSY, ABSENCE), complex partial (EPILEPSY, COMPLEX PARTIAL), and other types may occur. The electroencephalographic abnormalities and seizures tend to resolve by puberty. The language disorder may also resolve although some individuals are left with severe language dysfunction, including APHASIA and auditory AGNOSIA. (From Menkes, Textbook of Child Neurology, 5th ed, pp749-50; J Child Neurol 1997 Nov;12(8):489-495).

ID

http://purl.bioontology.org/ontology/MESH/D018887

altLabel

Landau Kleffner Acquired Epileptiform Aphasia

Acquired Epileptic Aphasias

Acquired Childhoood Aphasia with Convulsive Disorder

Epileptiform Aphasias, Acquired

Acquired Epileptiform Aphasias

Epileptic Aphasias, Acquired

Syndrome, Landau-Kleffner

Aphasia, Acquired, With Convulsive Disorder

Landau Kleffner Syndrome

Acquired Aphasia with Convulsive Disorder

Aphasia, Acquired Epileptic

Aphasia, Epileptic, Acquired

Landau-Kleffner Acquired Epileptiform Aphasia

Epileptic Aphasia, Acquired

Acquired Epileptic Aphasia

Acquired Epileptiform Aphasia

Epileptiform Aphasia, Acquired

AQL

BL CF CI CL CN CO DG DH DI DT EC EH EM EN EP ET GE HI IM ME MI MO NU PA PC PP PS PX RH RT SU TH UR VE VI

cui

C0282512

DC

1

definition

A syndrome characterized by the onset of isolated language dysfunction in otherwise normal children (age of onset 4-7 years) and epileptiform discharges on ELECTROENCEPHALOGRAPHY. Seizures, including atypical absence (EPILEPSY, ABSENCE), complex partial (EPILEPSY, COMPLEX PARTIAL), and other types may occur. The electroencephalographic abnormalities and seizures tend to resolve by puberty. The language disorder may also resolve although some individuals are left with severe language dysfunction, including APHASIA and auditory AGNOSIA. (From Menkes, Textbook of Child Neurology, 5th ed, pp749-50; J Child Neurol 1997 Nov;12(8):489-495).

DX

19960101

FX

D001037

HN

1996

Inverse of AQ

http://purl.bioontology.org/ontology/MESH/Q000097

http://purl.bioontology.org/ontology/MESH/Q000178

http://purl.bioontology.org/ontology/MESH/Q000175

http://purl.bioontology.org/ontology/MESH/Q000628

http://purl.bioontology.org/ontology/MESH/Q000276

http://purl.bioontology.org/ontology/MESH/Q000134

http://purl.bioontology.org/ontology/MESH/Q000139

http://purl.bioontology.org/ontology/MESH/Q000266

http://purl.bioontology.org/ontology/MESH/Q000378

http://purl.bioontology.org/ontology/MESH/Q000517

http://purl.bioontology.org/ontology/MESH/Q000662

http://purl.bioontology.org/ontology/MESH/Q000469

http://purl.bioontology.org/ontology/MESH/Q000151

http://purl.bioontology.org/ontology/MESH/Q000150

http://purl.bioontology.org/ontology/MESH/Q000821

http://purl.bioontology.org/ontology/MESH/Q000191

http://purl.bioontology.org/ontology/MESH/Q000196

http://purl.bioontology.org/ontology/MESH/Q000473

http://purl.bioontology.org/ontology/MESH/Q000145

http://purl.bioontology.org/ontology/MESH/Q000382

http://purl.bioontology.org/ontology/MESH/Q000451

http://purl.bioontology.org/ontology/MESH/Q000453

http://purl.bioontology.org/ontology/MESH/Q000534

http://purl.bioontology.org/ontology/MESH/Q000532

http://purl.bioontology.org/ontology/MESH/Q000503

http://purl.bioontology.org/ontology/MESH/Q000188

http://purl.bioontology.org/ontology/MESH/Q000235

http://purl.bioontology.org/ontology/MESH/Q000201

http://purl.bioontology.org/ontology/MESH/Q000209

http://purl.bioontology.org/ontology/MESH/Q000208

http://purl.bioontology.org/ontology/MESH/Q000601

http://purl.bioontology.org/ontology/MESH/Q000000981

http://purl.bioontology.org/ontology/MESH/Q000652

http://purl.bioontology.org/ontology/MESH/Q000523

http://purl.bioontology.org/ontology/MESH/Q000401

Inverse of RO

http://purl.bioontology.org/ontology/MESH/D001037

Machine permutation

1996

MDA

19941227

MMR

20170224

MN

C10.228.140.490.493.500

notation

D018887

prefLabel

Landau-Kleffner Syndrome

TERMUI

T764292

T056297

T764293

T368882

T056299

T056298

T812297

T368881

TH

NLM (1996)

OMIM (2013)

NLM (2000)

NLM (2011)

ORD (2010)

tui

T047

subClassOf

http://purl.bioontology.org/ontology/MESH/D000073376

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http://purl.bioontology.org/ontology/MSHFRE/D018887 MSHFRE CUI
http://purl.bioontology.org/ontology/SNOMEDCT/230438007 SNOMEDCT CUI
http://purl.bioontology.org/ontology/NDFRT/N0000003874 NDFRT CUI
http://purl.bioontology.org/ontology/MDRFRE/10052075 MDRFRE CUI
http://purl.bioontology.org/ontology/MEDDRA/10052075 MEDDRA CUI
http://purl.bioontology.org/ontology/SCTSPA/230438007 SCTSPA CUI
http://purl.bioontology.org/ontology/MDRGER/10052075 MDRGER CUI
http://purl.bioontology.org/ontology/MEDDRA/10052083 MEDDRA CUI
http://purl.bioontology.org/ontology/ICD10CM/G40.8 ICD10CM CUI
http://purl.bioontology.org/ontology/RCD/X006o RCD CUI
http://purl.bioontology.org/ontology/OMIM/245570 OMIM CUI
http://purl.bioontology.org/ontology/OMIM/138253 OMIM CUI
http://purl.bioontology.org/ontology/MDRGER/10052083 MDRGER CUI
http://purl.bioontology.org/ontology/MDRFRE/10052083 MDRFRE CUI
http://purl.bioontology.org/ontology/ICD10/F80.3 ICD10 CUI
http://www.ebi.ac.uk/efo/EFO_1001010 EFO LOOM
http://purl.obolibrary.org/obo/DOID_2538 DOID LOOM
http://www.case.edu/EpilepsyOntology.owl#AcquiredEpilepticAphasia EPSO LOOM
http://purl.obolibrary.org/obo/MONDO_0009509 MONDO LOOM
http://www.semanticweb.org/administrator/ontologies/2022/0/untitled-ontology-34#OWLClass59e389e5_819c_4e4a_bec1_5fa7d88af533 WWECA LOOM
http://www.semanticweb.org/ontologies/2009/3/EpilepsyOntology.owl#Landau-Kleffner_syndrome EPILONT LOOM
http://www.semanticweb.org/ontologies/2009/3/EpilepsyOntology.owl#Landau-Kleffner_syndrome MEPO LOOM
http://www.limics.org/hrdo/rdfns#pat_id_13835 HRDO LOOM
http://purl.obolibrary.org/obo/DOID_2538 BAO LOOM
http://purl.obolibrary.org/obo/DOID_2538 EPIO LOOM
http://purl.obolibrary.org/obo/DOID_2538 HHEAR LOOM
http://purl.obolibrary.org/obo/DOID_2538 NIFSTD LOOM
http://purl.obolibrary.org/obo/DOID_2538 MIDO LOOM
http://purl.obolibrary.org/obo/DOID_2538 FNS-H LOOM
http://www.orpha.net/ORDO/Orphanet_98818 ORDO LOOM
http://sbmi.uth.tmc.edu/ontology/ochv#C0282512 OCHV LOOM
http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#Landau-Kleffner_Syndrome CSEO LOOM
http://purl.bioontology.org/ontology/MEDDRA/10052083 MEDDRA LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#C10.228.140.490.535 RH-MESH LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#D018887 RH-MESH LOOM
http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C84806 NCIT LOOM
http://cbmi.med.harvard.edu/asdphenotype#Class_449 ASDPTO LOOM
http://purl.obolibrary.org/obo/OMIT_0019016 OMIT LOOM
http://purl.jp/bio/4/id/200906052382169332 IOBC LOOM
http://sbmi.uth.tmc.edu/ontology/ochv#27624 OCHV LOOM
http://www.owl-ontologies.com/NPOntology.owl#DOID_2538 NATPRO LOOM
http://uri.neuinfo.org/nif/nifstd/birnlex_12747 NIFDYS LOOM
http://uri.neuinfo.org/nif/nifstd/birnlex_12747 NIFSTD LOOM
http://purl.obolibrary.org/obo/MONDO_0009509 DOVES LOOM
http://purl.obolibrary.org/obo/NCIT_C84806 BERO LOOM
http://id.nlm.nih.gov/mesh/D018887 MDM LOOM
http://www.phoc.org.cn/pmo/class/PMO_00038248 PMAPP-PMO LOOM
http://bioontology.org/projects/ontologies/birnlex#birnlex_12747 BIRNLEX LOOM