Preferred Name |
Polyradiculoneuropathy, Chronic Inflammatory Demyelinating |
|
Synonyms |
Chronic Inflammatory Polyradiculoneuropathies |
|
Definitions |
A slowly progressive autoimmune demyelinating disease of peripheral nerves and nerve roots. Clinical manifestations include weakness and sensory loss in the extremities and enlargement of peripheral nerves. The course may be relapsing-remitting or demonstrate a step-wise progression. Protein is usually elevated in the spinal fluid and cranial nerves are typically spared. GUILLAIN-BARRE SYNDROME features a relatively rapid progression of disease which distinguishes it from this condition. (Adams et al., Principles of Neurology, 6th ed, p1337) |
|
ID |
http://purl.bioontology.org/ontology/MESH/D020277 |
|
altLabel |
Chronic Inflammatory Polyradiculoneuropathies Polyradiculoneuropathies, Chronic Inflammatory Chronic Inflammatory Polyradiculopathy Inflammatory Polyradiculopathies, Chronic Inflammatory Polyradiculoneuropathies, Chronic Chronic Inflammatory Demyelinating Polyradiculoneuropathy Inflammatory Polyradiculoneuropathy, Chronic Polyneuropathy, Inflammatory Demyelinating, Chronic Chronic Inflammatory Polyradiculoneuropathy Chronic Inflammatory Polyradiculopathies Polyradiculopathy, Chronic Inflammatory Polyradiculoneuropathy, Chronic Inflammatory Inflammatory Polyradiculopathy, Chronic CIDP Polyradiculopathies, Chronic Inflammatory |
|
AN |
do not confuse entry term CHRONIC INFLAMMATORY POLYRADICULONEUROPATHY with POLYRADICULONEUROPATHY, ACUTE INFLAMMATORY see GUILLAIN-BARRE SYNDROME |
|
AQL |
BL CF CI CL CN CO DG DH DI DT EC EH EM EN EP ET GE HI IM ME MI MO NU PA PC PP PS PX RH RT SU TH UR VE VI |
|
cui |
C0393819 |
|
DC |
1 |
|
definition |
A slowly progressive autoimmune demyelinating disease of peripheral nerves and nerve roots. Clinical manifestations include weakness and sensory loss in the extremities and enlargement of peripheral nerves. The course may be relapsing-remitting or demonstrate a step-wise progression. Protein is usually elevated in the spinal fluid and cranial nerves are typically spared. GUILLAIN-BARRE SYNDROME features a relatively rapid progression of disease which distinguishes it from this condition. (Adams et al., Principles of Neurology, 6th ed, p1337) |
|
DX |
20000101 |
|
HN |
2000 |
|
Inverse of AQ |
http://purl.bioontology.org/ontology/MESH/Q000097 http://purl.bioontology.org/ontology/MESH/Q000178 http://purl.bioontology.org/ontology/MESH/Q000175 http://purl.bioontology.org/ontology/MESH/Q000628 http://purl.bioontology.org/ontology/MESH/Q000276 http://purl.bioontology.org/ontology/MESH/Q000134 http://purl.bioontology.org/ontology/MESH/Q000139 http://purl.bioontology.org/ontology/MESH/Q000266 http://purl.bioontology.org/ontology/MESH/Q000378 http://purl.bioontology.org/ontology/MESH/Q000517 http://purl.bioontology.org/ontology/MESH/Q000662 http://purl.bioontology.org/ontology/MESH/Q000469 http://purl.bioontology.org/ontology/MESH/Q000151 http://purl.bioontology.org/ontology/MESH/Q000150 http://purl.bioontology.org/ontology/MESH/Q000821 http://purl.bioontology.org/ontology/MESH/Q000191 http://purl.bioontology.org/ontology/MESH/Q000196 http://purl.bioontology.org/ontology/MESH/Q000473 http://purl.bioontology.org/ontology/MESH/Q000145 http://purl.bioontology.org/ontology/MESH/Q000382 http://purl.bioontology.org/ontology/MESH/Q000451 http://purl.bioontology.org/ontology/MESH/Q000453 http://purl.bioontology.org/ontology/MESH/Q000534 http://purl.bioontology.org/ontology/MESH/Q000532 http://purl.bioontology.org/ontology/MESH/Q000503 http://purl.bioontology.org/ontology/MESH/Q000188 http://purl.bioontology.org/ontology/MESH/Q000235 http://purl.bioontology.org/ontology/MESH/Q000201 http://purl.bioontology.org/ontology/MESH/Q000209 http://purl.bioontology.org/ontology/MESH/Q000208 http://purl.bioontology.org/ontology/MESH/Q000601 http://purl.bioontology.org/ontology/MESH/Q000000981 http://purl.bioontology.org/ontology/MESH/Q000652 |
|
Machine permutation |
2000 |
|
MDA |
19991105 |
|
MMR |
20210312 |
|
MN |
C23.550.291.500.813 C10.668.829.800.750.600 C10.314.750.700 C10.114.750.175 C20.111.258.750.800 |
|
notation |
D020277 |
|
prefLabel |
Polyradiculoneuropathy, Chronic Inflammatory Demyelinating |
|
TERMUI |
T358266 T368457 T368461 T368459 T368460 T812350 T368458 |
|
TH |
OMIM (2013) NLM (2000) |
|
tui |
T047 |
|
subClassOf |