Medical Subject Headings

Last uploaded: January 16, 2025

Id	http://purl.bioontology.org/ontology/MESH/D054990 http://purl.bioontology.org/ontology/MESH/D054990
Preferred Name	Idiopathic Pulmonary Fibrosis
Definitions	A common interstitial lung disease of unknown etiology, usually occurring between 50-70 years of age. Clinically, it is characterized by an insidious onset of breathlessness with exertion and a nonproductive cough, leading to progressive DYSPNEA. Pathological features show scant interstitial inflammation, patchy collagen fibrosis, prominent fibroblast proliferation foci, and microscopic honeycomb change.
Synonyms	Idiopathic Pulmonary Fibroses Fibrocystic Pulmonary Dysplasias Usual Interstitial Pneumonitis Fibrocystic Pulmonary Dysplasia Pneumonitides, Usual Interstitial Pneumonitis, Usual Interstitial Cryptogenic Fibrosing Alveolitides Usual Interstitial Pneumonias Usual Interstitial Pneumonitides Pulmonary Fibrosis, Idiopathic Usual Interstitial Pneumonia Pulmonary Fibroses, Idiopathic Idiopathic Pulmonary Fibrosis, Familial Dysplasia, Fibrocystic Pulmonary Interstitial Pneumonia, Usual Familial Idiopathic Pulmonary Fibrosis Idiopathic Fibrosing Alveolitis, Chronic Form Pulmonary Dysplasia, Fibrocystic Fibrosing Alveolitides, Cryptogenic Interstitial Pneumonitis, Usual Fibrosing Alveolitis, Cryptogenic Cryptogenic Fibrosing Alveolitis See more See less
Type	http://www.w3.org/2002/07/owl#Class

definition	A common interstitial lung disease of unknown etiology, usually occurring between 50-70 years of age. Clinically, it is characterized by an insidious onset of breathlessness with exertion and a nonproductive cough, leading to progressive DYSPNEA. Pathological features show scant interstitial inflammation, patchy collagen fibrosis, prominent fibroblast proliferation foci, and microscopic honeycomb change.
altLabel	Idiopathic Pulmonary Fibroses Fibrocystic Pulmonary Dysplasias Usual Interstitial Pneumonitis Fibrocystic Pulmonary Dysplasia Pneumonitides, Usual Interstitial Pneumonitis, Usual Interstitial Cryptogenic Fibrosing Alveolitides Usual Interstitial Pneumonias Usual Interstitial Pneumonitides Pulmonary Fibrosis, Idiopathic Usual Interstitial Pneumonia Pulmonary Fibroses, Idiopathic Idiopathic Pulmonary Fibrosis, Familial Dysplasia, Fibrocystic Pulmonary Interstitial Pneumonia, Usual Familial Idiopathic Pulmonary Fibrosis Idiopathic Fibrosing Alveolitis, Chronic Form Pulmonary Dysplasia, Fibrocystic Fibrosing Alveolitides, Cryptogenic Interstitial Pneumonitis, Usual Fibrosing Alveolitis, Cryptogenic Cryptogenic Fibrosing Alveolitis See more See less
prefLabel	Idiopathic Pulmonary Fibrosis
TH	OMIM (2013) NLM (2009) GHR (2014) ORD (2010)
notation	D054990
DX	20090101
Machine permutation	2009
MN	C08.381.483.652.500
MMR	20220428
AQL	BL CF CI CL CN CO DG DH DI DT EC EH EM EN EP ET GE HI IM ME MI MO NU PA PC PP PS PX RH RT SU TH UR VE VI
HN	2009
subClassOf	http://purl.bioontology.org/ontology/MESH/D011658
Semantic type UMLS property	http://purl.bioontology.org/ontology/STY/T047
DC	1
MDA	20080708
type	http://www.w3.org/2002/07/owl#Class
tui	T047
cui	C4721952 C4721509 C1800706
AN	PULMONARY FIBROSIS is also available
Inverse of AQ	http://purl.bioontology.org/ontology/MESH/Q000097 http://purl.bioontology.org/ontology/MESH/Q000178 http://purl.bioontology.org/ontology/MESH/Q000175 http://purl.bioontology.org/ontology/MESH/Q000628 http://purl.bioontology.org/ontology/MESH/Q000276 http://purl.bioontology.org/ontology/MESH/Q000134 http://purl.bioontology.org/ontology/MESH/Q000139 http://purl.bioontology.org/ontology/MESH/Q000266 http://purl.bioontology.org/ontology/MESH/Q000378 http://purl.bioontology.org/ontology/MESH/Q000517 http://purl.bioontology.org/ontology/MESH/Q000662 http://purl.bioontology.org/ontology/MESH/Q000469 http://purl.bioontology.org/ontology/MESH/Q000151 http://purl.bioontology.org/ontology/MESH/Q000150 http://purl.bioontology.org/ontology/MESH/Q000821 http://purl.bioontology.org/ontology/MESH/Q000191 http://purl.bioontology.org/ontology/MESH/Q000196 http://purl.bioontology.org/ontology/MESH/Q000473 http://purl.bioontology.org/ontology/MESH/Q000145 http://purl.bioontology.org/ontology/MESH/Q000382 http://purl.bioontology.org/ontology/MESH/Q000451 http://purl.bioontology.org/ontology/MESH/Q000453 http://purl.bioontology.org/ontology/MESH/Q000534 http://purl.bioontology.org/ontology/MESH/Q000532 http://purl.bioontology.org/ontology/MESH/Q000503 http://purl.bioontology.org/ontology/MESH/Q000188 http://purl.bioontology.org/ontology/MESH/Q000235 http://purl.bioontology.org/ontology/MESH/Q000201 http://purl.bioontology.org/ontology/MESH/Q000209 http://purl.bioontology.org/ontology/MESH/Q000208 http://purl.bioontology.org/ontology/MESH/Q000601 http://purl.bioontology.org/ontology/MESH/Q000000981 http://purl.bioontology.org/ontology/MESH/Q000652 http://purl.bioontology.org/ontology/MESH/Q000523 http://purl.bioontology.org/ontology/MESH/Q000401 See more See less
TERMUI	T833800 T812635 T703058 T703056 T703057 T812633 T812634 T812632 T833799 T843517 See more See less

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