Medical Subject Headings

Last uploaded: January 31, 2024
Preferred Name

Amyotrophic Lateral Sclerosis

Synonyms

ALS Amyotrophic Lateral Sclerosis

Definitions

A degenerative disorder affecting upper MOTOR NEURONS in the brain and lower motor neurons in the brain stem and SPINAL CORD. Disease onset is usually after the age of 50 and the process is usually fatal within 3 to 6 years. Clinical manifestations include progressive weakness, atrophy, FASCICULATION, hyperreflexia, DYSARTHRIA, dysphagia, and eventual paralysis of respiratory function. Pathologic features include the replacement of motor neurons with fibrous ASTROCYTES and atrophy of anterior SPINAL NERVE ROOTS and corticospinal tracts. (From Adams et al., Principles of Neurology, 6th ed, pp1089-94)

ID

http://purl.bioontology.org/ontology/MESH/D000690

altLabel

ALS Amyotrophic Lateral Sclerosis

Lou-Gehrigs Disease

Disease, Guam

Lou Gehrig's Disease

Lou Gehrig Disease

Amyotrophic Lateral Sclerosis With Dementia

Gehrig Disease

Amyotrophic Lateral Sclerosis, Parkinsonism-Dementia Complex of Guam

Guam Form of Amyotrophic Lateral Sclerosis

Disease, Lou-Gehrigs

Motor Neuron Disease, Amyotrophic Lateral Sclerosis

ALS - Amyotrophic Lateral Sclerosis

Amyotrophic Lateral Sclerosis Parkinsonism Dementia Complex 1

Amyotrophic Lateral Sclerosis, Parkinsonism Dementia Complex of Guam

Gehrig's Disease

Gehrigs Disease

Amyotrophic Lateral Sclerosis, Guam Form

Charcot Disease

Dementia With Amyotrophic Lateral Sclerosis

Sclerosis, Amyotrophic Lateral

Amyotrophic Lateral Sclerosis-Parkinsonism-Dementia Complex 1

Guam Disease

AQL

BL CF CI CL CN CO DG DH DI DT EC EH EM EN EP ET GE HI IM ME MI MO NU PA PC PP PS PX RH RT SU TH UR VE VI

cui

C0002736

C0393554

C0543859

DC

1

definition

A degenerative disorder affecting upper MOTOR NEURONS in the brain and lower motor neurons in the brain stem and SPINAL CORD. Disease onset is usually after the age of 50 and the process is usually fatal within 3 to 6 years. Clinical manifestations include progressive weakness, atrophy, FASCICULATION, hyperreflexia, DYSARTHRIA, dysphagia, and eventual paralysis of respiratory function. Pathologic features include the replacement of motor neurons with fibrous ASTROCYTES and atrophy of anterior SPINAL NERVE ROOTS and corticospinal tracts. (From Adams et al., Principles of Neurology, 6th ed, pp1089-94)

DX

19660101

Inverse of AQ

http://purl.bioontology.org/ontology/MESH/Q000097

http://purl.bioontology.org/ontology/MESH/Q000178

http://purl.bioontology.org/ontology/MESH/Q000175

http://purl.bioontology.org/ontology/MESH/Q000628

http://purl.bioontology.org/ontology/MESH/Q000276

http://purl.bioontology.org/ontology/MESH/Q000134

http://purl.bioontology.org/ontology/MESH/Q000139

http://purl.bioontology.org/ontology/MESH/Q000266

http://purl.bioontology.org/ontology/MESH/Q000378

http://purl.bioontology.org/ontology/MESH/Q000517

http://purl.bioontology.org/ontology/MESH/Q000662

http://purl.bioontology.org/ontology/MESH/Q000469

http://purl.bioontology.org/ontology/MESH/Q000151

http://purl.bioontology.org/ontology/MESH/Q000150

http://purl.bioontology.org/ontology/MESH/Q000821

http://purl.bioontology.org/ontology/MESH/Q000191

http://purl.bioontology.org/ontology/MESH/Q000196

http://purl.bioontology.org/ontology/MESH/Q000473

http://purl.bioontology.org/ontology/MESH/Q000145

http://purl.bioontology.org/ontology/MESH/Q000382

http://purl.bioontology.org/ontology/MESH/Q000451

http://purl.bioontology.org/ontology/MESH/Q000453

http://purl.bioontology.org/ontology/MESH/Q000534

http://purl.bioontology.org/ontology/MESH/Q000532

http://purl.bioontology.org/ontology/MESH/Q000503

http://purl.bioontology.org/ontology/MESH/Q000188

http://purl.bioontology.org/ontology/MESH/Q000235

http://purl.bioontology.org/ontology/MESH/Q000201

http://purl.bioontology.org/ontology/MESH/Q000209

http://purl.bioontology.org/ontology/MESH/Q000208

http://purl.bioontology.org/ontology/MESH/Q000601

http://purl.bioontology.org/ontology/MESH/Q000000981

http://purl.bioontology.org/ontology/MESH/Q000652

http://purl.bioontology.org/ontology/MESH/Q000523

http://purl.bioontology.org/ontology/MESH/Q000401

Mapped from

http://purl.bioontology.org/ontology/MESH/C564688

http://purl.bioontology.org/ontology/MESH/C566288

http://purl.bioontology.org/ontology/MESH/C563895

http://purl.bioontology.org/ontology/MESH/C564300

http://purl.bioontology.org/ontology/MESH/C567699

http://purl.bioontology.org/ontology/MESH/C566290

http://purl.bioontology.org/ontology/MESH/C531617

http://purl.bioontology.org/ontology/MESH/C538251

http://purl.bioontology.org/ontology/MESH/C567429

http://purl.bioontology.org/ontology/MESH/C567244

http://purl.bioontology.org/ontology/MESH/C565955

http://purl.bioontology.org/ontology/MESH/C565956

http://purl.bioontology.org/ontology/MESH/C565957

http://purl.bioontology.org/ontology/MESH/C566550

http://purl.bioontology.org/ontology/MESH/C567499

http://purl.bioontology.org/ontology/MESH/C566576

MDA

19990101

MMR

20190429

MN

C18.452.845.800.050

C10.668.467.250

C10.574.562.250

C10.574.950.050

C10.228.854.139

notation

D000690

prefLabel

Amyotrophic Lateral Sclerosis

TERMUI

T366066

T814256

T840894

T366063

T002090

T366064

T000953133

T366069

T782950

T366067

T845605

T002092

T002091

T753625

T366068

TH

BIOETHICS (1998)

NLM (2000)

NLM (1966)

NLM (2020)

NLM (1990)

NLM (2012)

NLM (2013)

NLM (2010)

GHR (2014)

NLM (2014)

ORD (2010)

tui

T047

subClassOf

http://purl.bioontology.org/ontology/MESH/D057177

http://purl.bioontology.org/ontology/MESH/D013118

http://purl.bioontology.org/ontology/MESH/D016472

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