Medical Subject Headings

Last uploaded: January 31, 2024
Preferred Name

Pheochromocytoma

Synonyms

Extra-Adrenal Pheochromocytomas

Pheochromocytoma, Extra-Adrenal

Extra-Adrenal Pheochromocytoma

Pheochromocytomas, Extra-Adrenal

Pheochromocytomas

Pheochromocytoma, Extra Adrenal

Definitions

A usually benign, well-encapsulated, lobular, vascular tumor of chromaffin tissue of the ADRENAL MEDULLA or sympathetic paraganglia. The cardinal symptom, reflecting the increased secretion of EPINEPHRINE and NOREPINEPHRINE, is HYPERTENSION, which may be persistent or intermittent. During severe attacks, there may be HEADACHE; SWEATING, palpitation, apprehension, TREMOR; PALLOR or FLUSHING of the face, NAUSEA and VOMITING, pain in the CHEST and ABDOMEN, and paresthesias of the extremities. The incidence of malignancy is as low as 5% but the pathologic distinction between benign and malignant pheochromocytomas is not clear. (Dorland, 27th ed; DeVita Jr et al., Cancer: Principles & Practice of Oncology, 3d ed, p1298)

ID

http://purl.bioontology.org/ontology/MESH/D010673

altLabel

Extra-Adrenal Pheochromocytomas

Pheochromocytoma, Extra-Adrenal

Extra-Adrenal Pheochromocytoma

Pheochromocytomas, Extra-Adrenal

Pheochromocytomas

Pheochromocytoma, Extra Adrenal

AN

benign or malignant; coord IM with usually ADRENAL GLAND NEOPLASMS (IM)

AQL

BL BS CF CH CI CL CN CO DG DH DI DT EC EH EM EN EP ET GE HI IM ME MI MO NU PA PC PP PS PX RH RT SC SU TH UL UR VE VI

cui

C0031511

C1257877

DC

1

definition

A usually benign, well-encapsulated, lobular, vascular tumor of chromaffin tissue of the ADRENAL MEDULLA or sympathetic paraganglia. The cardinal symptom, reflecting the increased secretion of EPINEPHRINE and NOREPINEPHRINE, is HYPERTENSION, which may be persistent or intermittent. During severe attacks, there may be HEADACHE; SWEATING, palpitation, apprehension, TREMOR; PALLOR or FLUSHING of the face, NAUSEA and VOMITING, pain in the CHEST and ABDOMEN, and paresthesias of the extremities. The incidence of malignancy is as low as 5% but the pathologic distinction between benign and malignant pheochromocytomas is not clear. (Dorland, 27th ed; DeVita Jr et al., Cancer: Principles & Practice of Oncology, 3d ed, p1298)

DX

19660101

FX

D018813

D018814

Inverse of AQ

http://purl.bioontology.org/ontology/MESH/Q000097

http://purl.bioontology.org/ontology/MESH/Q000098

http://purl.bioontology.org/ontology/MESH/Q000178

http://purl.bioontology.org/ontology/MESH/Q000175

http://purl.bioontology.org/ontology/MESH/Q000628

http://purl.bioontology.org/ontology/MESH/Q000648

http://purl.bioontology.org/ontology/MESH/Q000276

http://purl.bioontology.org/ontology/MESH/Q000134

http://purl.bioontology.org/ontology/MESH/Q000139

http://purl.bioontology.org/ontology/MESH/Q000266

http://purl.bioontology.org/ontology/MESH/Q000378

http://purl.bioontology.org/ontology/MESH/Q000517

http://purl.bioontology.org/ontology/MESH/Q000662

http://purl.bioontology.org/ontology/MESH/Q000469

http://purl.bioontology.org/ontology/MESH/Q000151

http://purl.bioontology.org/ontology/MESH/Q000150

http://purl.bioontology.org/ontology/MESH/Q000821

http://purl.bioontology.org/ontology/MESH/Q000191

http://purl.bioontology.org/ontology/MESH/Q000196

http://purl.bioontology.org/ontology/MESH/Q000473

http://purl.bioontology.org/ontology/MESH/Q000145

http://purl.bioontology.org/ontology/MESH/Q000737

http://purl.bioontology.org/ontology/MESH/Q000382

http://purl.bioontology.org/ontology/MESH/Q000451

http://purl.bioontology.org/ontology/MESH/Q000453

http://purl.bioontology.org/ontology/MESH/Q000534

http://purl.bioontology.org/ontology/MESH/Q000532

http://purl.bioontology.org/ontology/MESH/Q000503

http://purl.bioontology.org/ontology/MESH/Q000188

http://purl.bioontology.org/ontology/MESH/Q000235

http://purl.bioontology.org/ontology/MESH/Q000201

http://purl.bioontology.org/ontology/MESH/Q000209

http://purl.bioontology.org/ontology/MESH/Q000208

http://purl.bioontology.org/ontology/MESH/Q000601

http://purl.bioontology.org/ontology/MESH/Q000000981

http://purl.bioontology.org/ontology/MESH/Q000556

http://purl.bioontology.org/ontology/MESH/Q000652

http://purl.bioontology.org/ontology/MESH/Q000523

http://purl.bioontology.org/ontology/MESH/Q000401

Inverse of RO

http://purl.bioontology.org/ontology/MESH/D018814

http://purl.bioontology.org/ontology/MESH/D018813

Mapped from

http://purl.bioontology.org/ontology/MESH/C531777

http://purl.bioontology.org/ontology/MESH/C563522

http://purl.bioontology.org/ontology/MESH/C566807

MDA

19990101

MMR

20120703

MN

C04.557.465.625.650.700.725

C04.557.580.625.650.700.725

notation

D010673

prefLabel

Pheochromocytoma

TERMUI

T530045

T031545

TH

OMIM (2013)

NLM (2004)

NLM (1966)

ORD (2010)

tui

T191

subClassOf

http://purl.bioontology.org/ontology/MESH/D010235

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Delete Mapping To Ontology Source
http://purl.bioontology.org/ontology/MSHFRE/D010673 MSHFRE CUI
http://purl.bioontology.org/ontology/MSHFRE/D010673 MSHFRE CUI
http://purl.bioontology.org/ontology/SNMI/M-87000 SNMI CUI
http://purl.bioontology.org/ontology/OMIM/608537 OMIM CUI
http://purl.bioontology.org/ontology/NDFRT/N0000002390 NDFRT CUI
http://purl.bioontology.org/ontology/PDQ/CDR0000039816 PDQ CUI
http://purl.bioontology.org/ontology/OMIM/185470 OMIM CUI
http://purl.bioontology.org/ontology/MEDLINEPLUS/C0031511 MEDLINEPLUS CUI
http://purl.bioontology.org/ontology/OMIM/MTHU015027 OMIM CUI
http://purl.bioontology.org/ontology/MSHFRE/D010235 MSHFRE CUI
http://purl.bioontology.org/ontology/WHOFRE/1116 WHOFRE CUI
http://purl.bioontology.org/ontology/OMIM/602690 OMIM CUI
http://purl.bioontology.org/ontology/OMIM/164761 OMIM CUI
http://purl.bioontology.org/ontology/OMIM/171300 OMIM CUI
http://purl.bioontology.org/ontology/ICPC2P/T73008 ICPC2P CUI
http://purl.bioontology.org/ontology/WHO/1116 WHO-ART CUI
http://purl.bioontology.org/ontology/CST/NEOPL COSTART CUI
http://purl.bioontology.org/ontology/OMIM/MTHU004455 OMIM CUI
http://purl.bioontology.org/ontology/OMIM/MTHU067043 OMIM CUI
http://purl.bioontology.org/ontology/SNOMEDCT/302835009 SNOMEDCT LOOM
http://sbmi.uth.tmc.edu/ontology/ochv#C0031511 OCHV LOOM
http://nanbyodata.jp/ontology/NANDO_2200078 NANDO LOOM
http://purl.bioontology.org/ontology/SNOMEDCT/85583005 SNOMEDCT LOOM
http://purl.bioontology.org/ontology/MEDDRA/10034876 MEDDRA LOOM
http://purl.jp/bio/4/id/200906031583220746 IOBC LOOM
http://purl.obolibrary.org/obo/DERMO_0002049 DERMO LOOM
http://sbmi.uth.tmc.edu/ontology/ochv#9623 OCHV LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#C04.557.465.625.650.700.725 RH-MESH LOOM
http://bmi.utah.edu/ontologies/hfontology/C0031511 HFO LOOM
http://radlex.org/RID/RID4516 RADLEX LOOM
http://purl.bioontology.org/ontology/PDQ/CDR0000039816 PDQ LOOM
http://purl.obolibrary.org/obo/DOID_0050771 DOID LOOM
http://purl.obolibrary.org/obo/DOID_0050771 BAO LOOM
http://purl.obolibrary.org/obo/DOID_0050771 HHEAR LOOM
http://purl.obolibrary.org/obo/DOID_0050771 NIFSTD LOOM
http://purl.obolibrary.org/obo/DOID_0050771 MIDO LOOM
http://purl.obolibrary.org/obo/DOID_0050771 FNS-H LOOM
http://purl.org/obo/owl/HP#HP_0002666 BDO LOOM
http://purl.obolibrary.org/obo/OMIM_171300 CCO LOOM
http://purl.obolibrary.org/obo/OGMD_0000048 OGMD LOOM
http://www.phoc.org.cn/pmo/class/PMO_00085364 PMAPP-PMO LOOM
http://www.semanticweb.org/ontologies/2012/11/abnormalities.owl#phenodb:2458 IFAR LOOM
http://purl.obolibrary.org/obo/MONDO_0008233 MONDO LOOM
http://purl.obolibrary.org/obo/MONDO_0008233 DOVES LOOM
http://purl.obolibrary.org/obo/MPATH_377 MPATH LOOM
http://purl.obolibrary.org/obo/MPATH_377 UPHENO LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#D010673 RH-MESH LOOM
http://purl.obolibrary.org/obo/OMIT_0011661 OMIT LOOM
http://purl.bioontology.org/ontology/MEDLINEPLUS/C0031511 MEDLINEPLUS LOOM
http://purl.bioontology.org/ontology/OMIM/MTHU015027 OMIM LOOM
http://www.semanticweb.org/ontologies/2012/11/abnormalities.owl#phenodb:2311 IFAR LOOM
http://purl.bioontology.org/ontology/OMIM/171300 OMIM LOOM
http://doe-generated-ontology.com/OntoAD#C0031511 ONTOAD LOOM
http://purl.bioontology.org/ontology/CSP/2012-7663 CRISP LOOM
http://purl.bioontology.org/ontology/ICPC2P/T73008 ICPC2P LOOM
http://www.gamuts.net/entity#pheochromocytoma GAMUTS LOOM
http://identifiers.org/omim/171300 REXO LOOM
http://identifiers.org/omim/171300 GEXO LOOM
http://identifiers.org/omim/171300 RETO LOOM
http://purl.obolibrary.org/obo/HP_0002666 HP LOOM
http://purl.obolibrary.org/obo/HP_0002666 UPHENO LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#C04.557.580.625.650.700.725 RH-MESH LOOM
http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#Pheochromocytoma CSEO LOOM