loading...| Preferred Name |
Malignant Atrophic Papulosis [Disease/Finding] |
|
| Synonyms |
Degos's Malignant Atrophic Papulosis |
|
| ID |
http://purl.bioontology.org/ontology/NDFRT/N0000181064 |
|
| altLabel |
Degos's Malignant Atrophic Papulosis Papulosis, Malignant Atrophic Malignant Atrophic Papulosis Erythrokeratoderma en cocardes Kohlmeier-Degos Disease Degos Syndrome Degos Disease |
|
| cui |
C0221011 |
|
| MESH DEFINITION |
Variously described as a vasculopathy, endovasculitis, or occlusive arteriopathy, this condition occurs in a benign cutaneous form and a lethal multiorgan systemic variant. It is characterized by a narrowing and occlusion of the lumen of small to medium-sized blood vessels, leading to ischemia and infarction in the involved organ systems. The etiology and pathophysiology are unknown. |
|
| MESH DUI |
D054853 |
|
| MeSH name |
Malignant Atrophic Papulosis |
|
| MESH UI |
M0508347 |
|
| NDFRT kind |
DISEASE_KIND |
|
| notation |
N0000181064 |
|
| NUI |
N0000181064 |
|
| prefLabel |
Malignant Atrophic Papulosis [Disease/Finding] |
|
| tui |
T047 |
|
| subClassOf |