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SNOMED CT
Last uploaded:
January 16, 2025
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Id | http://purl.bioontology.org/ontology/SNOMEDCT/234437005
http://purl.bioontology.org/ontology/SNOMEDCT/234437005
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Preferred Name | Hemophagocytic lymphohistiocytosis |
Synonyms |
Hemophagocytic syndrome
Haemophagocytic syndrome
Hemophagocytic lymphohistiocytosis (disorder)
Hyperinflammatory lymphohistiocytosis
Haemophagocytic lymphohistiocytosis
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Type | http://www.w3.org/2002/07/owl#Class |
All Properties
altLabel |
Hemophagocytic syndrome
Haemophagocytic syndrome
Hemophagocytic lymphohistiocytosis (disorder)
Hyperinflammatory lymphohistiocytosis
Haemophagocytic lymphohistiocytosis
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prefLabel | Hemophagocytic lymphohistiocytosis
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Type ID |
900000000000003001
900000000000013009
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CASE SIGNIFICANCE ID | 900000000000448009
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notation | 234437005
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Effective time | 20020131
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Active | 1
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Has finding site | |
Has pathological process | |
subClassOf | |
Semantic type UMLS property | |
type | |
Subset member | 6011000124106~MAPRULE~IFA 1197594000 | Periodic fever, infantile enterocolitis, autoinflammatory syndrome | AND IFA 445518008 | Age at onset of clinical finding (observable entity) | < 29.0 days
447562003~MAPADVICE~ALWAYS D76.1
447562003~MAPRULE~TRUE
6011000124106~MAPTARGET~D76.1
6011000124106~MAPADVICE~IF PERIODIC FEVER, INFANTILE ENTEROCOLITIS, AUTOINFLAMMATORY SYNDROME AND IF AGE AT ONSET OF CLINICAL FINDING BEFORE 29.0 DAYS CHOOSE P78.89 | MAP OF SOURCE CONCEPT IS CONTEXT DEPENDENT
6011000124106~MAPTARGET~D76.2
6011000124106~MAPPRIORITY~7
6011000124106~MAPPRIORITY~4
6011000124106~MAPADVICE~MAP SOURCE CONCEPT CANNOT BE CLASSIFIED WITH AVAILABLE DATA
6011000124106~MAPADVICE~IF ACQUIRED HEMOPHAGOCYTIC LYMPHOHISTIOCYTOSIS ASSOCIATED WITH MALIGNANT DISEASE CHOOSE C80.1 | MAP OF SOURCE CONCEPT IS CONTEXT DEPENDENT
6011000124106~MAPTARGET~
6011000124106~MAPCATEGORYID~447638001
900000000000497000~MAPTARGET~X20E8
6011000124106~MAPGROUP~1
6011000124106~MAPGROUP~2
6011000124106~MAPADVICE~IF INFECTION-ASSOCIATED MACROPHAGE ACTIVATION SYNDROME CHOOSE D76.2 | CONSIDER ADDITIONAL CODE TO IDENTIFY SPECIFIC CONDITION OR DISEASE | MAP OF SOURCE CONCEPT IS CONTEXT DEPENDENT
6011000124106~MAPTARGET~B20
6011000124106~MAPRULE~IFA 713444005 | Hemophagocytic syndrome co-occurrent with human immunodeficiency virus infection |
900000000000508004~ACCEPTABILITYID~900000000000549004
6011000124106~MAPADVICE~IF PERIODIC FEVER, INFANTILE ENTEROCOLITIS, AUTOINFLAMMATORY SYNDROME CHOOSE M04.9 | MAP OF SOURCE CONCEPT IS CONTEXT DEPENDENT
6011000124106~MAPADVICE~IF HEMOPHAGOCYTIC SYNDROME CO-OCCURRENT WITH HUMAN IMMUNODEFICIENCY VIRUS INFECTION CHOOSE B20 | CONSIDER ADDITIONAL CODE TO IDENTIFY SPECIFIC CONDITION OR DISEASE | MAP OF SOURCE CONCEPT IS CONTEXT DEPENDENT
6011000124106~MAPADVICE~IF PERIODIC FEVER, INFANTILE ENTEROCOLITIS, AUTOINFLAMMATORY SYNDROME CHOOSE K52.9 | MAP OF SOURCE CONCEPT IS CONTEXT DEPENDENT
6011000124106~MAPTARGET~M08.20
447562003~MAPGROUP~1
6011000124106~MAPADVICE~IF MACROPHAGE ACTIVATION SYNDROME DUE TO JUVENILE SYSTEMIC ONSET ARTHRITIS CHOOSE M08.20 | CONSIDER ADDITIONAL CODE TO IDENTIFY SPECIFIC CONDITION OR DISEASE | MAP OF SOURCE CONCEPT IS CONTEXT DEPENDENT
447562003~CORRELATIONID~447561005
6011000124106~MAPADVICE~IF HEMOPHAGOCYTIC LYMPHOHISTIOCYTOSIS DUE TO INFECTION CHOOSE D76.2 | CONSIDER ADDITIONAL CODE TO IDENTIFY SPECIFIC CONDITION OR DISEASE | MAP OF SOURCE CONCEPT IS CONTEXT DEPENDENT
6011000124106~MAPCATEGORYID~447637006
900000000000509007~ACCEPTABILITYID~900000000000548007
6011000124106~MAPRULE~IFA 1290500002 | Infection-associated macrophage activation syndrome |
6011000124106~MAPADVICE~IF ACQUIRED HEMOPHAGOCYTIC LYMPHOHISTIOCYTOSIS ASSOCIATED WITH MALIGNANT DISEASE CHOOSE D76.1 | MAP OF SOURCE CONCEPT IS CONTEXT DEPENDENT
6011000124106~MAPTARGET~M04.1
900000000000508004~ACCEPTABILITYID~900000000000548007
6011000124106~MAPRULE~IFA 713444005 | Hemophagocytic syndrome with human immunodeficiency virus infection |
6011000124106~MAPADVICE~IF MACROPHAGE ACTIVATION SYNDROME DUE TO JUVENILE SYSTEMIC ONSET ARTHRITIS CHOOSE D76.1 | MAP OF SOURCE CONCEPT IS CONTEXT DEPENDENT
6011000124106~MAPADVICE~IF HEMOPHAGOCYTIC SYNDROME CO-OCCURRENT WITH HUMAN IMMUNODEFICIENCY VIRUS INFECTION CHOOSE D76.2 | CONSIDER ADDITIONAL CODE TO IDENTIFY SPECIFIC CONDITION OR DISEASE | MAP OF SOURCE CONCEPT IS CONTEXT DEPENDENT
447562003~MAPPRIORITY~1
6011000124106~MAPADVICE~IF PERIODIC FEVER, INFANTILE ENTEROCOLITIS, AUTOINFLAMMATORY SYNDROME CHOOSE M04.1 | MAP OF SOURCE CONCEPT IS CONTEXT DEPENDENT
6011000124106~MAPTARGET~C80.1
447562003~MAPCATEGORYID~447637006
6011000124106~MAPRULE~IFA 1197594000 | Periodic fever, infantile enterocolitis, autoinflammatory syndrome |
6011000124106~MAPTARGET~M04.9
6011000124106~MAPADVICE~ALWAYS D76.1
6011000124106~MAPRULE~OTHERWISE TRUE
6011000124106~MAPPRIORITY~5
6011000124106~MAPADVICE~IF HEMOPHAGOCYTIC SYNDROME WITH HUMAN IMMUNODEFICIENCY VIRUS INFECTION CHOOSE B20 | CONSIDER ADDITIONAL CODE TO IDENTIFY SPECIFIC CONDITION OR DISEASE | MAP OF SOURCE CONCEPT IS CONTEXT DEPENDENT
6011000124106~MAPRULE~IFA 190959006 | Hemophagocytic lymphohistiocytosis due to infection |
6011000124106~MAPRULE~IFA 782915004 | Acquired hemophagocytic lymphohistiocytosis associated with malignant disease |
6011000124106~MAPCATEGORYID~447639009
6011000124106~MAPPRIORITY~1
6011000124106~MAPRULE~IFA 1156801007 | Macrophage activation syndrome due to juvenile systemic onset arthritis |
6011000124106~MAPPRIORITY~6
6011000124106~CORRELATIONID~447561005
6011000124106~MAPRULE~TRUE
6011000124106~MAPTARGET~K52.9
6011000124106~MAPGROUP~3
6011000124106~MAPPRIORITY~3
900000000000509007~ACCEPTABILITYID~900000000000549004
6011000124106~MAPADVICE~IF HEMOPHAGOCYTIC SYNDROME WITH HUMAN IMMUNODEFICIENCY VIRUS INFECTION CHOOSE D76.2 | CONSIDER ADDITIONAL CODE TO IDENTIFY SPECIFIC CONDITION OR DISEASE | MAP OF SOURCE CONCEPT IS CONTEXT DEPENDENT
6011000124106~MAPTARGET~P78.89
6011000124106~MAPPRIORITY~2
447562003~MAPTARGET~D76.1
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DEFINITION STATUS ID | 900000000000074008
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tui | T047
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CTV3ID | X20E8
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cui | C0024291
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Has associated morphology |
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