Preferred Name |
Double outlet right ventricle |
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Synonyms |
Transposition of great vessels, interventricular septal defect AND overriding aorta Origin of both great vessels from right ventricle |
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ID |
http://purl.bioontology.org/ontology/SNOMEDCT/7484005 |
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Active |
1 |
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altLabel |
Transposition of great vessels, interventricular septal defect AND overriding aorta Double outlet right ventricle (disorder) Taussig-Bing defect Taussig-Bing syndrome DORV - Double outlet right ventricle Origin of both great vessels from right ventricle |
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CASE SIGNIFICANCE ID |
900000000000020002 900000000000448009 900000000000017005 |
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CTV3ID |
P511. |
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cui |
C0013069 C1956413 |
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DEFINITION STATUS ID |
900000000000074008 |
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Effective time |
20020131 |
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Has associated morphology | ||
Has finding site | ||
Has pathological process | ||
INACTIVATION INDICATOR |
900000000000494007 |
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notation |
7484005 |
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Occurs in | ||
prefLabel |
Double outlet right ventricle |
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Subset member |
6011000124106~MAPRULE~IFA 253298003 | Double outlet right ventricle with subaortic ventricular septal defect (disorder) | 447562003~MAPTARGET~Q20.1 6011000124106~MAPADVICE~IF DOUBLE OUTLET RIGHT VENTRICLE WITH SUBPULMONARY VENTRICULAR SEPTAL DEFECT CHOOSE Q20.1 | MAP OF SOURCE CONCEPT IS CONTEXT DEPENDENT 6011000124106~MAPADVICE~ALWAYS Q20.1 6011000124106~MAPRULE~IFA 871601006 | Double outlet right ventricle with subaortic ventricular septal defect and pulmonary stenosis Fallot type | 447562003~MAPRULE~TRUE 6011000124106~MAPADVICE~IF DOUBLE OUTLET RIGHT VENTRICLE WITH SUBAORTIC VENTRICULAR SEPTAL DEFECT AND PULMONARY STENOSIS FALLOT TYPE CHOOSE Q20.1 | MAP OF SOURCE CONCEPT IS CONTEXT DEPENDENT 6011000124106~MAPRULE~IFA 253300003 | Double outlet right ventricle with doubly committed ventricular septal defect (disorder) | 6011000124106~MAPRULE~IFA 840507004 | Double outlet right ventricle with subaortic ventricular septal defect without pulmonary stenosis | 6011000124106~MAPPRIORITY~7 6011000124106~MAPTARGET~Q22.1 6011000124106~MAPPRIORITY~4 6011000124106~MAPTARGET~Q21.0 6011000124106~MAPADVICE~IF DOUBLE OUTLET RIGHT VENTRICLE WITH DOUBLY COMMITTED VENTRICULAR SEPTAL DEFECT AND PULMONARY STENOSIS CHOOSE Q22.1 | MAP OF SOURCE CONCEPT IS CONTEXT DEPENDENT 6011000124106~MAPADVICE~MAP SOURCE CONCEPT CANNOT BE CLASSIFIED WITH AVAILABLE DATA 900000000000490003~VALUEID~900000000000494007 6011000124106~MAPTARGET~ 6011000124106~MAPCATEGORYID~447638001 6011000124106~MAPGROUP~1 6011000124106~MAPGROUP~2 6011000124106~MAPADVICE~IF DOUBLE OUTLET RIGHT VENTRICLE WITH SUBAORTIC OR DOUBLY COMMITTED VENTRICULAR SEPTAL DEFECT AND PULMONARY STENOSIS FALLOT TYPE CHOOSE Q20.1 | MAP OF SOURCE CONCEPT IS CONTEXT DEPENDENT 6011000124106~MAPPRIORITY~10 6011000124106~MAPPRIORITY~8 6011000124106~MAPRULE~IFA 762251008 | Double outlet right ventricle with subaortic or doubly committed ventricular septal defect without pulmonary stenosis - ventricular septal defect type | 900000000000508004~ACCEPTABILITYID~900000000000549004 447562003~MAPGROUP~1 6011000124106~MAPADVICE~IF DOUBLE OUTLET RIGHT VENTRICLE WITH SUBAORTIC VENTRICULAR SEPTAL DEFECT CHOOSE Q21.0 | MAP OF SOURCE CONCEPT IS CONTEXT DEPENDENT 447562003~CORRELATIONID~447561005 6011000124106~MAPADVICE~IF DOUBLE OUTLET RIGHT VENTRICLE WITH SUBAORTIC VENTRICULAR SEPTAL DEFECT WITHOUT PULMONARY STENOSIS CHOOSE Q21.0 | MAP OF SOURCE CONCEPT IS CONTEXT DEPENDENT 6011000124106~MAPADVICE~IF DOUBLE OUTLET RIGHT VENTRICLE WITH NONCOMMITTED VENTRICULAR SEPTAL DEFECT CHOOSE Q21.0 | MAP OF SOURCE CONCEPT IS CONTEXT DEPENDENT 6011000124106~MAPRULE~IFA 253299006 | Double outlet right ventricle with noncommitted ventricular septal defect (disorder) | 6011000124106~MAPCATEGORYID~447637006 900000000000509007~ACCEPTABILITYID~900000000000548007 6011000124106~MAPADVICE~IF DOUBLE OUTLET RIGHT VENTRICLE WITH SUBAORTIC VENTRICULAR SEPTAL DEFECT AND PULMONARY STENOSIS FALLOT TYPE CHOOSE Q22.1 | MAP OF SOURCE CONCEPT IS CONTEXT DEPENDENT 6011000124106~MAPADVICE~IF DOUBLE OUTLET RIGHT VENTRICLE WITH SUBAORTIC OR DOUBLY COMMITTED VENTRICULAR SEPTAL DEFECT AND PULMONARY STENOSIS FALLOT TYPE CHOOSE Q22.1 | MAP OF SOURCE CONCEPT IS CONTEXT DEPENDENT 6011000124106~MAPADVICE~IF DOUBLE OUTLET RIGHT VENTRICLE WITH DOUBLY COMMITTED VENTRICULAR SEPTAL DEFECT CHOOSE Q21.0 | MAP OF SOURCE CONCEPT IS CONTEXT DEPENDENT 6011000124106~MAPADVICE~IF DOUBLE OUTLET RIGHT VENTRICLE WITH SUBPULMONARY VENTRICULAR SEPTAL DEFECT CHOOSE Q21.0 | MAP OF SOURCE CONCEPT IS CONTEXT DEPENDENT 6011000124106~MAPADVICE~IF DOUBLE OUTLET RIGHT VENTRICLE WITH SUBAORTIC VENTRICULAR SEPTAL DEFECT CHOOSE Q20.1 | MAP OF SOURCE CONCEPT IS CONTEXT DEPENDENT 900000000000508004~ACCEPTABILITYID~900000000000548007 6011000124106~MAPADVICE~IF DOUBLE OUTLET RIGHT VENTRICLE WITH DOUBLY COMMITTED VENTRICULAR SEPTAL DEFECT CHOOSE Q20.1 | MAP OF SOURCE CONCEPT IS CONTEXT DEPENDENT 6011000124106~MAPADVICE~IF DOUBLE OUTLET RIGHT VENTRICLE WITH SUBAORTIC OR DOUBLY COMMITTED VENTRICULAR SEPTAL DEFECT WITHOUT PULMONARY STENOSIS - VENTRICULAR SEPTAL DEFECT TYPE CHOOSE Q20.1 | MAP OF SOURCE CONCEPT IS CONTEXT DEPENDENT 6011000124106~MAPADVICE~IF DOUBLE OUTLET RIGHT VENTRICLE WITH SUBAORTIC VENTRICULAR SEPTAL DEFECT WITHOUT PULMONARY STENOSIS CHOOSE Q20.1 | MAP OF SOURCE CONCEPT IS CONTEXT DEPENDENT 6011000124106~MAPADVICE~IF DOUBLE OUTLET RIGHT VENTRICLE WITH SUBAORTIC OR DOUBLY COMMITTED VENTRICULAR SEPTAL DEFECT WITHOUT PULMONARY STENOSIS - VENTRICULAR SEPTAL DEFECT TYPE CHOOSE Q21.0 | MAP OF SOURCE CONCEPT IS CONTEXT DEPENDENT 6011000124106~MAPADVICE~IF DOUBLE OUTLET RIGHT VENTRICLE WITH SUBAORTIC OR DOUBLY COMMITTED VENTRICULAR SEPTAL DEFECT AND PULMONARY STENOSIS FALLOT TYPE CHOOSE Q21.0 | MAP OF SOURCE CONCEPT IS CONTEXT DEPENDENT 447562003~MAPPRIORITY~1 6011000124106~MAPRULE~IFA 448794008 | Double outlet right ventricle with subpulmonary ventricular septal defect | 447562003~MAPCATEGORYID~447637006 6011000124106~MAPRULE~IFA 448516008 | Double outlet right ventricle with doubly committed ventricular septal defect and pulmonary stenosis | 6011000124106~MAPRULE~OTHERWISE TRUE 6011000124106~MAPPRIORITY~5 6011000124106~MAPRULE~IFA 448794008 | Double outlet right ventricle with subpulmonary ventricular septal defect (disorder) | 6011000124106~MAPRULE~IFA 871599009 | Double outlet right ventricle with subaortic or doubly committed ventricular septal defect and pulmonary stenosis Fallot type | 6011000124106~MAPPRIORITY~9 6011000124106~MAPCATEGORYID~447639009 6011000124106~MAPRULE~IFA 253299006 | Double outlet right ventricle with noncommitted ventricular septal defect | 900000000000497000~MAPTARGET~P511. 6011000124106~MAPRULE~IFA 448516008 | Double outlet right ventricle with doubly committed ventricular septal defect and pulmonary stenosis (disorder) | 6011000124106~MAPTARGET~Q20.1 6011000124106~MAPPRIORITY~1 6011000124106~MAPRULE~IFA 253300003 | Double outlet right ventricle with doubly committed ventricular septal defect | 6011000124106~MAPPRIORITY~6 6011000124106~CORRELATIONID~447561005 900000000000531004~TARGETCOMPONENT~448794008 447562003~MAPADVICE~ALWAYS Q20.1 6011000124106~MAPRULE~TRUE 6011000124106~MAPADVICE~IF DOUBLE OUTLET RIGHT VENTRICLE WITH NONCOMMITTED VENTRICULAR SEPTAL DEFECT CHOOSE Q20.1 | MAP OF SOURCE CONCEPT IS CONTEXT DEPENDENT 6011000124106~MAPADVICE~IF DOUBLE OUTLET RIGHT VENTRICLE WITH DOUBLY COMMITTED VENTRICULAR SEPTAL DEFECT AND PULMONARY STENOSIS CHOOSE Q21.0 | MAP OF SOURCE CONCEPT IS CONTEXT DEPENDENT 6011000124106~MAPGROUP~3 6011000124106~MAPPRIORITY~3 6011000124106~MAPRULE~IFA 253298003 | Double outlet right ventricle with subaortic ventricular septal defect | 6011000124106~MAPADVICE~IF DOUBLE OUTLET RIGHT VENTRICLE WITH DOUBLY COMMITTED VENTRICULAR SEPTAL DEFECT AND PULMONARY STENOSIS CHOOSE Q20.1 | MAP OF SOURCE CONCEPT IS CONTEXT DEPENDENT 900000000000509007~ACCEPTABILITYID~900000000000549004 6011000124106~MAPPRIORITY~2 |
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tui |
T019 |
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Type ID |
900000000000003001 900000000000013009 |
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subClassOf |