SNOMED CT

Last uploaded: January 31, 2024
Preferred Name

Chordoma

Synonyms

Chordoma (disorder)

Definitions

A rare malignant neoplasm arising from embryonic remnants of the notochord in axial skeleton. The neoplasm is predominantly found in adults. The clinical presentation depends entirely on the location of the chordoma. The main possible locations are the sacrum, intracranially at the clivus and along the spinal axis. Chordoma has characteristics of slow growth, with local destruction of the bone and extension into the adjacent soft tissue.

ID

http://purl.bioontology.org/ontology/SNOMEDCT/1156453008

Active

1

altLabel

Chordoma (disorder)

CASE SIGNIFICANCE ID

900000000000448009

CTV3ID

XVG7m

cui

C0008487

definition

A rare malignant neoplasm arising from embryonic remnants of the notochord in axial skeleton. The neoplasm is predominantly found in adults. The clinical presentation depends entirely on the location of the chordoma. The main possible locations are the sacrum, intracranially at the clivus and along the spinal axis. Chordoma has characteristics of slow growth, with local destruction of the bone and extension into the adjacent soft tissue.

DEFINITION STATUS ID

900000000000073002

Effective time

20210731

Has associated morphology

http://purl.bioontology.org/ontology/SNOMEDCT/50007008

notation

1156453008

prefLabel

Chordoma

Subset member

447562003~MAPRULE~TRUE

6011000124106~MAPPRIORITY~4

6011000124106~MAPGROUP~1

6011000124106~MAPADVICE~IF PRIMARY CHORDOMA OF BONE OF SKULL CHOOSE C41.0 | MAP OF SOURCE CONCEPT IS CONTEXT DEPENDENT

447562003~MAPGROUP~1

447562003~CORRELATIONID~447561005

6011000124106~MAPCATEGORYID~447637006

6011000124106~MAPRULE~IFA 130891000119106 | Chordoma of coccyx |

900000000000509007~ACCEPTABILITYID~900000000000548007

6011000124106~MAPADVICE~ALWAYS C41.2

447562003~MAPADVICE~ALWAYS C80.9 | POSSIBLE REQUIREMENT FOR MORPHOLOGY CODE

6011000124106~MAPTARGET~C41.4

900000000000508004~ACCEPTABILITYID~900000000000548007

6011000124106~MAPRULE~IFA 130941000119107 | Primary chordoma of bone of skull |

447562003~MAPTARGET~C80.9

6011000124106~MAPADVICE~IF CHORDOMA OF SACRUM CHOOSE C41.4 | MAP OF SOURCE CONCEPT IS CONTEXT DEPENDENT

447562003~MAPPRIORITY~1

6011000124106~MAPRULE~IFA 447730004 | Chordoma of sacrum |

447562003~MAPCATEGORYID~447637006

6011000124106~MAPRULE~OTHERWISE TRUE

6011000124106~MAPPRIORITY~5

6011000124106~MAPTARGET~C41.2

6011000124106~MAPRULE~IFA 130911000119108 | Chordoma of pelvis |

6011000124106~MAPCATEGORYID~447639009

6011000124106~MAPADVICE~IF CHORDOMA OF COCCYX CHOOSE C41.4 | MAP OF SOURCE CONCEPT IS CONTEXT DEPENDENT

6011000124106~MAPPRIORITY~1

6011000124106~CORRELATIONID~447561005

6011000124106~MAPADVICE~ALWAYS C41.2 | DESCENDANTS NOT EXHAUSTIVELY MAPPED

6011000124106~MAPTARGET~C41.0

6011000124106~MAPRULE~TRUE

900000000000497000~MAPTARGET~XVG7m

6011000124106~MAPPRIORITY~3

6011000124106~MAPADVICE~IF CHORDOMA OF PELVIS CHOOSE C41.4 | MAP OF SOURCE CONCEPT IS CONTEXT DEPENDENT

6011000124106~MAPPRIORITY~2

tui

T191

Type ID

900000000000003001

900000000000013009

subClassOf

http://purl.bioontology.org/ontology/SNOMEDCT/363346000

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Delete Mapping To Ontology Source
http://purl.bioontology.org/ontology/MSHFRE/D002817 MSHFRE CUI
http://purl.bioontology.org/ontology/CSP/2000-4323 CRISP CUI
http://purl.bioontology.org/ontology/MEDDRA/10008747 MEDDRA CUI
http://purl.bioontology.org/ontology/SCTSPA/50007008 SCTSPA CUI
http://purl.bioontology.org/ontology/MDRFRE/10008747 MDRFRE CUI
http://purl.bioontology.org/ontology/SCTSPA/1156453008 SCTSPA CUI
http://purl.bioontology.org/ontology/OMIM/MTHU031495 OMIM CUI
http://purl.bioontology.org/ontology/PDQ/CDR0000040402 PDQ CUI
http://purl.bioontology.org/ontology/RCD/BBa5. RCD CUI
http://purl.bioontology.org/ontology/MESH/D002817 MESH CUI
http://purl.bioontology.org/ontology/NDFRT/N0000000771 NDFRT CUI
http://purl.bioontology.org/ontology/MDRGER/10008747 MDRGER CUI
http://purl.bioontology.org/ontology/SNMI/M-93703 SNMI CUI
http://purl.obolibrary.org/obo/DOID_3302 DOID LOOM
http://purl.obolibrary.org/obo/MONDO_0008978 EFO LOOM
http://purl.obolibrary.org/obo/HP_0010762 EFO LOOM
http://purl.obolibrary.org/obo/DOID_3302 DOID LOOM
http://purl.obolibrary.org/obo/MONDO_0008978 MONDO LOOM
http://purl.obolibrary.org/obo/MPATH_405 ZP LOOM
http://purl.obolibrary.org/obo/HP_0010762 HP LOOM
http://purl.obolibrary.org/obo/OMIT_0004137 OMIT LOOM
http://purl.obolibrary.org/obo/MONDO_0008978 DOVES LOOM
http://www.owl-ontologies.com/NPOntology.owl#DOID_3302 NATPRO LOOM
http://www.phoc.org.cn/pmo/class/PMO_00085663 PMAPP-PMO LOOM
http://purl.bioontology.org/ontology/CSP/2000-4323 CRISP LOOM
http://www.limics.org/hrdo/rdfns#pat_id_6023 HRDO LOOM
http://purl.bioontology.org/ontology/MEDDRA/10008747 MEDDRA LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#D002817 RH-MESH LOOM
http://id.nlm.nih.gov/mesh/D002817 MDM LOOM
http://purl.obolibrary.org/obo/OMIM_215400 CCO LOOM
http://purl.obolibrary.org/obo/DOID_3302 BAO LOOM
http://purl.obolibrary.org/obo/DOID_3302 HHEAR LOOM
http://purl.obolibrary.org/obo/DOID_3302 NIFSTD LOOM
http://purl.obolibrary.org/obo/DOID_3302 MIDO LOOM
http://purl.obolibrary.org/obo/DOID_3302 FNS-H LOOM
http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#C2947 NCIT LOOM
http://www.semanticweb.org/ontologies/2012/11/abnormalities.owl#phenodb:2520 IFAR LOOM
http://sbmi.uth.tmc.edu/ontology/ochv#2906 OCHV LOOM
http://www.gamuts.net/entity#chordoma GAMUTS LOOM
http://purl.jp/bio/4/id/200906078632117383 IOBC LOOM
http://radlex.org/RID/RID4146 RADLEX LOOM
http://purl.bioontology.org/ontology/OMIM/MTHU031495 OMIM LOOM
http://purl.bioontology.org/ontology/PDQ/CDR0000040402 PDQ LOOM
http://purl.obolibrary.org/obo/MPATH_405 MPATH LOOM
http://purl.obolibrary.org/obo/MPATH_405 UPHENO LOOM
http://purl.bioontology.org/ontology/RCD/BBa5. RCD LOOM
http://phenomebrowser.net/ontologies/mesh/mesh.owl#C04.557.465.220 RH-MESH LOOM
http://purl.bioontology.org/ontology/MESH/D002817 MESH LOOM
http://sbmi.uth.tmc.edu/ontology/ochv#C0008487 OCHV LOOM
http://ncicb.nci.nih.gov/xml/owl/EVS/Thesaurus.owl#Chordoma CSEO LOOM
http://identifiers.org/omim/215400 REXO LOOM
http://identifiers.org/omim/215400 GEXO LOOM
http://identifiers.org/omim/215400 RETO LOOM
http://purl.obolibrary.org/obo/NCIT_C2947 BERO LOOM
http://purl.bioontology.org/ontology/SNMI/M-93703 SNMI LOOM
http://www.orpha.net/ORDO/Orphanet_178 ORDO LOOM
http://purl.obolibrary.org/obo/HP_0010762 UPHENO LOOM
http://scai.fraunhofer.de/CSEO#Chordoma CSEO LOOM