6011000124106~MAPADVICE~IF ENCEPHALOPATHY, INTRACEREBRAL CALCIFICATION, RETINAL DEGENERATION SYNDROME CHOOSE G93.40 | MAP OF SOURCE CONCEPT IS CONTEXT DEPENDENT
6011000124106~MAPADVICE~ALWAYS G93.89 | DESCENDANTS NOT EXHAUSTIVELY MAPPED
447562003~MAPADVICE~ALWAYS G93.8 | POSSIBLE REQUIREMENT FOR AN EXTERNAL CAUSE CODE
447562003~MAPRULE~TRUE
6011000124106~MAPTARGET~G40.909
6011000124106~MAPTARGET~G93.40
6011000124106~MAPPRIORITY~7
6011000124106~MAPADVICE~IF CRANIOSYNOSTOSIS AND INTRACRANIAL CALCIFICATION SYNDROME CHOOSE Q75.0 | MAP OF SOURCE CONCEPT IS CONTEXT DEPENDENT
6011000124106~MAPPRIORITY~4
6011000124106~MAPADVICE~IF RAMBAUD GALLIAN SYNDROME CHOOSE K92.89 | MAP OF SOURCE CONCEPT IS CONTEXT DEPENDENT
6011000124106~MAPTARGET~I67.89
6011000124106~MAPADVICE~MAP SOURCE CONCEPT CANNOT BE CLASSIFIED WITH AVAILABLE DATA
6011000124106~MAPTARGET~P91.819
6011000124106~MAPTARGET~
6011000124106~MAPCATEGORYID~447638001
6011000124106~MAPGROUP~1
6011000124106~MAPGROUP~2
6011000124106~MAPRULE~IFA 720816004 | Craniosynostosis and intracranial calcification syndrome (disorder) |
6011000124106~MAPRULE~IFA 733049004 | Encephalopathy, intracerebral calcification, retinal degeneration syndrome |
6011000124106~MAPPRIORITY~8
6011000124106~MAPADVICE~IF RAMBAUD GALLIAN SYNDROME CHOOSE G93.89 | MAP OF SOURCE CONCEPT IS CONTEXT DEPENDENT
6011000124106~MAPADVICE~IF RAMBAUD GALLIAN SYNDROME CHOOSE H34.9 | MAP OF SOURCE CONCEPT IS CONTEXT DEPENDENT
6011000124106~MAPADVICE~IF ENCEPHALOPATHY, INTRACEREBRAL CALCIFICATION, RETINAL DEGENERATION SYNDROME CHOOSE G93.89 | MAP OF SOURCE CONCEPT IS CONTEXT DEPENDENT
6011000124106~MAPADVICE~IF ENCEPHALOPATHY, INTRACEREBRAL CALCIFICATION, RETINAL DEGENERATION SYNDROME AND IF AGE AT ONSET OF CLINICAL FINDING BEFORE 29.0 DAYS CHOOSE P91.819 | MAP OF SOURCE CONCEPT IS CONTEXT DEPENDENT
6011000124106~MAPTARGET~Q75.0
447562003~MAPGROUP~1
447562003~CORRELATIONID~447561005
6011000124106~MAPCATEGORYID~447637006
6011000124106~MAPADVICE~IF CEREBRORETINAL MICROANGIOPATHY WITH CALCIFICATIONS AND CYSTS CHOOSE G93.89 | MAP OF SOURCE CONCEPT IS CONTEXT DEPENDENT
900000000000509007~ACCEPTABILITYID~900000000000548007
6011000124106~MAPTARGET~G23.8
6011000124106~MAPRULE~IFA 722386009 | Celiac disease with epilepsy and cerebral calcification syndrome |
900000000000508004~ACCEPTABILITYID~900000000000548007
6011000124106~MAPADVICE~IF CELIAC DISEASE WITH EPILEPSY AND CEREBRAL CALCIFICATION SYNDROME CHOOSE K90.0 | CONSIDER ADDITIONAL CODE TO IDENTIFY SPECIFIC CONDITION OR DISEASE | MAP OF SOURCE CONCEPT IS CONTEXT DEPENDENT
6011000124106~MAPADVICE~ALWAYS G93.89
6011000124106~MAPTARGET~H35.50
6011000124106~MAPADVICE~IF CEREBRORETINAL MICROANGIOPATHY WITH CALCIFICATIONS AND CYSTS CHOOSE G93.0 | MAP OF SOURCE CONCEPT IS CONTEXT DEPENDENT
6011000124106~MAPTARGET~H34.9
6011000124106~MAPADVICE~IF ENCEPHALOPATHY, INTRACEREBRAL CALCIFICATION, RETINAL DEGENERATION SYNDROME CHOOSE H35.50 | MAP OF SOURCE CONCEPT IS CONTEXT DEPENDENT
6011000124106~MAPADVICE~IF CELIAC DISEASE WITH EPILEPSY AND CEREBRAL CALCIFICATION SYNDROME CHOOSE G93.89 | MAP OF SOURCE CONCEPT IS CONTEXT DEPENDENT
447562003~MAPPRIORITY~1
6011000124106~MAPTARGET~G93.89
447562003~MAPCATEGORYID~447637006
6011000124106~MAPTARGET~K92.89
6011000124106~MAPRULE~OTHERWISE TRUE
6011000124106~MAPPRIORITY~5
6011000124106~MAPCATEGORYID~447639009
6011000124106~MAPRULE~IFA 110997000 | Fahr's syndrome (disorder) |
6011000124106~MAPPRIORITY~1
6011000124106~MAPPRIORITY~6
6011000124106~MAPADVICE~IF FAHR'S SYNDROME CHOOSE G23.8 | MAP OF SOURCE CONCEPT IS CONTEXT DEPENDENT
6011000124106~MAPADVICE~IF CEREBRORETINAL MICROANGIOPATHY WITH CALCIFICATIONS AND CYSTS CHOOSE I67.89 | CONSIDER ADDITIONAL CODE TO IDENTIFY SPECIFIC CONDITION OR DISEASE | MAP OF SOURCE CONCEPT IS CONTEXT DEPENDENT
6011000124106~MAPADVICE~IF CRANIOSYNOSTOSIS AND INTRACRANIAL CALCIFICATION SYNDROME CHOOSE G93.89 | MAP OF SOURCE CONCEPT IS CONTEXT DEPENDENT
6011000124106~CORRELATIONID~447561005
6011000124106~MAPRULE~IFA 711482008 | Cerebroretinal microangiopathy with calcifications and cysts (disorder) |
6011000124106~MAPRULE~IFA 720816004 | Craniosynostosis and intracranial calcification syndrome |
6011000124106~MAPTARGET~G93.0
6011000124106~MAPRULE~TRUE
6011000124106~MAPGROUP~3
6011000124106~MAPRULE~IFA 110997000 | Fahr's syndrome |
6011000124106~MAPRULE~IFA 711482008 | Cerebroretinal microangiopathy with calcifications and cysts |
6011000124106~MAPTARGET~K90.0
6011000124106~MAPPRIORITY~3
6011000124106~MAPRULE~IFA 722386009 | Celiac disease with epilepsy and cerebral calcification syndrome (disorder) |
447562003~MAPTARGET~G93.8
6011000124106~MAPPRIORITY~2
900000000000497000~MAPTARGET~F28y0
6011000124106~MAPRULE~IFA 724002003 | Rambaud Gallian syndrome |
6011000124106~MAPRULE~IFA 733049004 | Encephalopathy, intracerebral calcification, retinal degeneration syndrome | AND IFA 445518008 | Age at onset of clinical finding (observable entity) | < 29.0 days
6011000124106~MAPADVICE~IF CELIAC DISEASE WITH EPILEPSY AND CEREBRAL CALCIFICATION SYNDROME CHOOSE G40.909 | MAP OF SOURCE CONCEPT IS CONTEXT DEPENDENT
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